Kasabach-Merritt现象的研究进展和治疗  

Development and treatments of Kasabach-Merritt phenomenon

作　　者：龚毓宾 孙斌[1] 雷红召[1] 董长宪[1] 

机构地区：[1]河南省人民医院血管瘤科,郑州450052

出　　处：《中华实用儿科临床杂志》2014年第10期789-791,共3页Chinese Journal of Applied Clinical Pediatrics

基　　金：河南省科技攻关项目（112102310235）

摘　　要：Kasabach-Merritt现象（KMP）是快速生长的血管瘤伴消耗性凝血功能障碍的一类现象,多见于婴幼儿早期,好发于肢体远端、躯干部、腹膜后腔和颈部,其病死率高达30％.目前并无统一、有效的治疗方法.现综述KMP的病理生理学基础、诊断以及其治疗方法.Kasabach-Merritt phenomenon（KMP） is characterized by thrombocytopenia with enlarging vascular tumour, KMP usually develops in infancy and is associated with significant morbidity and mortality, the mortality rate is reported as high as 30%. It commonly reported sites of tumor include extremities, trunk, retroperitoneum and neck. There is no consensus in treatment and various regimens have been used by different authors. This report is aim to learn the pathoohvsiolo~ of the KMP and its diaznosis and treatment.

关 键 词：Kasabach-Merritt现象 血管瘤 血小板减少 消耗性凝血功能障碍 卡波西血管内皮瘤 簇状血管瘤 

分 类 号：R732.2[医药卫生—肿瘤]