Hallervorden-Spatz综合征的MRI诊断  

MRI diagnosis of Hallervorden-Spatz syndrome

作　　者：袁建军[1] 程文君[1] 康五根[1] 仲海[2] 

机构地区：[1]浙江省台州市立医院放射科,浙江台州318000 [2]山东大学第二医院影像科,山东济南250033

出　　处：《医学影像学杂志》2014年第6期902-905,共4页Journal of Medical Imaging

摘　　要：目的：探讨Hallervorden-Spatz综合征的颅脑M RI诊断价值，提高对该病的认识。方法回顾性分析2007年2月～2012年4月经临床证实为 Hallervorden-Spatz综合征的4例患者颅脑MRI资料。结果 Hallervorden-Spatz综合征颅脑M RI表现为：双侧苍白球、黑质T2 WI像对称性低信号，苍白球低信号的前内侧出现斑点状高信号，即典型的“虎眼征”。SWI像上病灶呈低信号，MRS检查可见NAA、NAA/Cr及Cho/Cr下降。结论 Hallervorden-Spatz综合征具有典型的MRI表现，MRI检查在Hallervorden-Spatz综合征中有重要的诊断价值。Objective To investigate the diagnostic value of MRI in Hallervorden-Spatz syndrome .Methods MRI data of Hallervorden-Spatz syndrome in 4 patients in our hospital from February 2007 to April 2012 were retrospectively analyzed .Results The brain MRI of Hallervorden-Spatz syndrome was demonstrated abnormalities confined to the pallidum , which presented diffuse low signal intensity in SWI ,and eye-of-the-tiger sign in T2 WI .Compared with the normal brain tissue ,the NAA ,NAA/Cr ,Cho/Cr were decreased .Conclusion Hallervorden-Spatz syndrome has definite MR imaging findings ,and M RI is of important value in diagnosis of Hallervorden-Spatz syndrome .

关 键 词：HALLERVORDEN-SPATZ综合征 磁共振成像 诊断 

分 类 号：R445.2[医药卫生—影像医学与核医学] R742[医药卫生—诊断学]