原发性肾脏恶性纤维组织细胞瘤(附4例报告)  

Primary Malignant Fibrous Histocytoma of Kidney-A Report of 4 Cases

作　　者：姚欣[1] 李文录[1] 孙保存[2] 刘素香[2] 张莉[1] 董立新[1] 马腾骧[3] 

机构地区：[1]天津医科大学附属肿瘤医院盆腔泌尿科,天津市300060 [2]天津医科大学附属肿瘤医院病理科,天津市300060 [3]天津市泌尿外科研究所

出　　处：《中国肿瘤临床》2001年第7期545-548,共4页Chinese Journal of Clinical Oncology

摘　　要：目的：探讨原发性肾脏恶性纤维组织细胞瘤的临床、病理特点，以及影响预后的相关因素。方法：分析临床所见4例肾恶性纤维组织细胞瘤（MFH），并总结国内外39例病例文献资料。结果：消瘦、肿块是肾MFH的常见临床症状，免疫组化检查有助于提高肾MFH病理诊断率，肾MFH预后与肿瘤病理类型及转移有关，与肿瘤大小无关。结论：肾MFH是极罕见的高度恶性肾原发肿瘤，盲目扩大手术范围对预后无明显改善。Objective To investigate the clinical pathological characteristics and prognostic factors of primary malignant fibrous histocytoma MFH． Methods Four cases of renal MFH in our hospital and other 39 cases reported at home and abroad were analysed and summarized． Results Emaciation and palpable mass were the common manifestations of renal MFH． Immunohistochemical examination was helpful for the diagnosis of renal MFH． The prognosis was associated with the pathological type and metastatic status of MFH but not with the size of tumor． Conclusion Renal MFH is a very rare highly malignant tumor． The prognosis can not be improved by blindly expanding the operative region．

关 键 词：肾脏恶性纤维组织细胞瘤 病理 预后 罕见类型 MFH 

分 类 号：R737.11[医药卫生—肿瘤]