儿童肝豆状核变性的MRI表现  

MR Imaging of Hepatolenticular Degeneration in Children

作　　者：高煜[1] 范国平[1] 冯斌[1] 刘明[1] 金彪[1] 王秋艳[1] 李玉华[1] 朱杰明[1] 

机构地区：[1]上海第二医科大学附属新华医院放射科,上海200092

出　　处：《中国医学影像技术》2002年第1期25-27,共3页Chinese Journal of Medical Imaging Technology

摘　　要：目的　探讨MRI在儿童肝豆状核变性中的诊断价值。方法　对 40例肝豆状核变性的儿童进行治疗前脑部及腹部的MRI检查。其中 12例治疗后进行了复查。结果　治疗前 40例MRI中 ,2 3例病人有脑部异常信号 ,16例病人肝内大量弥漫性结节状异常信号。 12例复查病例中 ,7例脑部的病变变小或消失。 6例肝脏病变消失。结论　MRI对肝豆状核变性的诊断及预后具有重要的意义。Objective To evaluate MRI in diagnosing hepatolenticular degeneration (HLD) in children. Methods Pretreatment brain and abdomen MRI were performed in 40 children with HLD. 12 patients who were treated were followed. Results Abnormal signals on brain MRI were seen in 23 cases, nodular abnormal signs on liver were seen in 16 cases. On the follow up MRI of 12 patients, brain lesions of 7 patients shrunk or disappeared, and liver lesions of 6 patients disappeared. Conclusion MRI is of great significance in making diagnosis and prognosis of HLD.

关 键 词：儿童 肝豆状核变性 MRI 脑部信号异常 

分 类 号：R742.404[医药卫生—神经病学与精神病学] R445.2[医药卫生—临床医学]