特发性黄斑视网膜血管扩张症2型的临床特点及诊断治疗研究进展  

Characteristics, multimodality imaging and treatment of macular telangiectasia type 2

作　　者：才艺 石璇[1] 赵明威[1] 黎晓新[1] Cai Yi;Shi Xuan;Zhao Mingwei;Li Xiaoxin(Department of Ophthalmology, Peking University People's Hospital, Key Laboratory of Vision Loss and Restoration, Ministry of Education, Beijing Key Laboratory of Diagnosis and Therapy of Retinal and Choroid Diseases, Beijing 100044, China)

机构地区：[1]北京大学人民医院眼科视觉损伤与修复教育部重点实验室、视网膜脉络膜疾病诊治研究北京市重点实验室,100044

出　　处：《中华眼科杂志》2019年第1期68-73,共6页Chinese Journal of Ophthalmology

摘　　要：特发性黄斑视网膜血管扩张症是一种特发的、非继发于炎性反应或阻塞等已知原因、以黄斑区毛细血管网异常扩张、周围微动脉和微静脉异常扩张以及神经纤维层萎缩为特征的双眼获得性疾病的总称,目前被广泛认为是一种黄斑区神经退行性疾病。本文针对特发性黄斑视网膜血管扩张症的流行病学特征、临床分型及特征、分期、发病机制以及治疗方法进行总结和分析,以期为临床深入研究和探讨提供参考。Macular telangiectasia type 2 (MacTel 2) is an idiopathic entity which is characterized by dilated capillary network near, or around, the fovea of the macula. The spectrums secondary to macular retinal vascular inflammation or obstruction are excluded. It is a binocular disease in general. MacTel 2 is now widely recognized as a macular neurodegenerative disease rather than a simple vascular disease. This article reviews the epidemiological features, clinical features, staging, special examinations, pathogenesis and treatment of MacTel 2.

关 键 词：视网膜毛细血管扩张症 室管膜细胞 体层摄影术 光学相干 荧光素血管造影术 

分 类 号：R774[医药卫生—眼科]