烟雾病:流行病学,病因,诊断及治疗(英文)  

Moyamoya disease:epidemiology,etiology,diagnosis and management

作　　者：黄正[1] 赵继宗[1] 

机构地区：[1]首都医科大学附属北京天坛医院神经外科,北京100050

出　　处：《转化医学研究（电子版）》2014年第2期1-7,共7页Translational Medicine Research(Electronic Edition)

摘　　要：烟雾病是一种不常见的脑血管病,发现至今已有40余年历史。该病以颈内动脉及主要分支进行性狭窄,伴侧枝循环形成(烟雾样血管)为主要特点。好发于5岁左右的儿童及40岁左右的成人,临床表现为缺血性及出血性卒中。脑血运重建手术可以改善烟雾病患者脑血流动力学状态,预防卒中再次发生。本文主要阐述烟雾病的流行病学、病因、临床特点及手术治疗。Moyamoya disease as an uncommon cerebrovascular disease has been known for more than 40 years.It is characterized by progressive stenosis of internal carotid artery and its main branches.There is compensatory development of collateral vessels,which are termed moyamoya vessels.Ischemic and hemorrhagic stroke can occur in both pediatric and adult patients.Surgical revascularization can improve cerebral hemodynamics and prevent further stroke.In this review,we discuss the epidemiology,etiology,clinical features and surgical treatment of moyamoya disease.

关 键 词：流行病学 手术治疗 烟雾病 病因 血流动力学状态 脑血管病 诊断 侧枝循环形成 

分 类 号：R743.3[医药卫生—神经病学与精神病学]