肺淋巴管肌瘤病的高分辨率CT表现  

High resolution CT findings of pulmonary lymphangioleiomyomatosis

作　　者：蔡庆国[1] 

机构地区：[1]山东省菏泽市立医院放射科,274031

出　　处：《中国医师进修杂志》2014年第27期28-31,共4页Chinese Journal of Postgraduates of Medicine

摘　　要：目的 探讨肺淋巴管肌瘤病的高分辨率CT（HRCT）特点,以提高对本病的诊断水平.方法 回顾性分析13例经病理证实的肺淋巴管肌瘤病患者胸部HRCT改变.结果 13例均为女性,年龄28 ～ 57岁,平均40岁.11例患者胸部HRCT表现为两肺均匀分布、多发的薄壁气囊影,直径数毫米至2 cm,囊壁厚1～2mm,气囊影无分布差异;囊腔周围为正常肺组织;2例患者弥漫分布大小不一囊腔、周围未见明显正常肺组织.1例患者左侧胸腔积液、腹膜后多发淋巴结肿大.结论 肺淋巴管肌瘤病的HRCT表现具有特征性,是诊断本病首选的影像学检查方法.Objective To discuss the high resolution CT （HRCT） characteristics of pulmonary lymphangioleiomyomatosis （PLAM）,and improve the diagnosis ability of the disease.Methods The pulmonary HRCT changes in 13 patients with pathology proved PLAM were retrospectively analyzed.Results The reported 13 cases of PLAM were all female,the average onset age was 40 （28-57） years old.HRCT showed bilateral,diffuse thin walled cysts throughout both lungs in 11 cases.The cystic air spaces ranged in diameter from a few millimeter to 2 cm,the thickness of the cyst walls was 1-2 mm,air bag cavity surrounded by normal lung tissue.Multiple well-defined cystic air spaces surrounded by uniformly thin wall in 2 cases,no normal lung tissue between the air cavity.One case had complications of left side pleural effusion and lymph nodes of multiple retroperitoneal.Conclusion The HRCT findings of PLAM has diagnostic performance,and it should be used as the first choice for the diagnosis of the disease.

关 键 词：肺 淋巴管肌瘤病 体层摄影术 X线计算机 

分 类 号：R734.2[医药卫生—肿瘤]