指状突树突细胞肉瘤的特征及诊断治疗  

Characteristics,diagnosis and treatment of interdigitating dendritic cell sarcoma

作　　者：李俊萍[1] 赵如森[1] 王永涛[1] 李兵[1] 张桂芝[1] 

机构地区：[1]山东省淄博市临淄区人民医院肿瘤科,255400

出　　处：《国际肿瘤学杂志》2014年第9期675-678,共4页Journal of International Oncology

摘　　要：指状突树突细胞肉瘤（IDCS）是一种极罕见的造血组织来源的树突细胞恶性肿瘤，主要表现为浅表淋巴结肿大，也可以发生于肺脏、肾脏、膀胱、胸膜等不典型的部位。随着病理诊断水平提高、免疫组织化学及电镜的应用，该病诊断检出率明显升高。目前手术仍是该病治疗的主要手段，但由于疾病恶性程度高、进展迅速，具有不良的预后。Interdigitating dendritic cell sarcoma （IDCS）is a rare malignant tumor of the dendritic cell, derived from the hematopoietic tissue.The major clinical manifestation of IDCS is superficial lymphadenopathy, and the enlarged lymph nodes may appear in some atypical ereas,such as the lung,kidney,bladder and the pleura,etc.With the development of the pathological diagnosis and the application of immunohistochemical staining and electron microscopes,the case detection rate is apparently improved.With the high degree of malignant,rapid progress and poor prognosis of the disease,currently,surgical therapy is still the main approach to the treatment of IDCS.

关 键 词：树突状细胞肉瘤 指突 诊断 治疗 

分 类 号：R733[医药卫生—肿瘤]