Parkes-Weber综合征伴假性Kaposi肉瘤一例  

A case of Parkes-Weber syndrome accompanied by pseudo-Kaposi＆#39;s sarcoma

作　　者：唐金玲[1] 树叶[1] 陈卫坚[1] 罗勇奇[1] 汤建萍[1] 

机构地区：[1]湖南省儿童医院皮肤科,长沙410007

出　　处：《中华皮肤科杂志》2014年第11期812-814,共3页Chinese Journal of Dermatology

摘　　要：患者女,8岁7个月.右臀部紫红色斑8年,右下肢较左下肢逐渐增大7年余,多发性赘生物1年.皮肤科检查：右下肢较左下肢肥大且长,皮肤鲜红斑痣,皮温增高及皮肤大量赘生物伴有恶臭.X线、磁共振成像、多普勒超声提示高流速脉管畸形.皮肤病理可见血管增生,成纤维细胞增生及红细胞外溢,诊断为伴假性Kaposi肉瘤的Parkes-Weber综合征.A girl who aged eight years and seven months presented with prunosus patches on the right buttock for 8 years,gradual unilateral enlargement of the right lower limb for more than 7 years,and multiple vegetations for 1 year.Dermatological examination showed nevus flammeus and multiple malodorous vegetations over the right lower limb with high skin temperature.The right lower limb was thicker and longer than the left lower limb.X-ray examination,magnetic resonance imaging and Doppler ultrasound examination revealed high-flow vascular malformations.Pathological examination of the vegetations showed vascular proliferation,fibroblast proliferation and erythrocyte extravasation.She was diagnosed as Parkes-Weber syndrome accompanied by pseudo-Kaposi＇s sarcoma.

关 键 词：Parkes-Weber综合征 假性KAPOSI肉瘤 动静脉瘘 

分 类 号：R739.5[医药卫生—肿瘤]