颅内Rosai-Dorfman病MRI表现并文献复习  

Intracranial Rosai-Dorfman disease: MRI findings and literature review

作　　者：袁菁[1] 高培毅[1] 

机构地区：[1]首都医科大学附属北京天坛医院放射科,北京100050

出　　处：《影像诊断与介入放射学》2015年第2期97-102,共6页Diagnostic Imaging & Interventional Radiology

摘　　要：目的总结颅内Rosai-Dorfman病(RDD)的MRI影像表现,提高对该病的认识。方法回顾性分析4例经病理确诊的颅内RDD患者的MRI影像表现,并复习相关中文文献。结果 4例颅内RDD中,2例表现为累及硬脑膜的单发或多发肿块,MRI T1WI呈等信号、T2WI为等-低信号,增强扫描多为均匀强化,伴有硬膜尾征。1例表现为同时累及硬脑膜和柔脑膜的肿块,增强扫描可见柔脑膜强化。1例表现为累及颅底、海绵窦、鼻窦、颞下窝的弥漫性病变。结论颅内RDD可分为硬脑膜型、硬脑膜+柔脑膜型、脑实质型、鞍区型、脑室型五种类型,硬脑膜型最常见。病变多表现为T2WI等-低信号,病变中心为T2WI更低信号,可能是本病的特征性信号表现。Objective To summarize the MR findings of intracranial Rosai-Dorfman Ddisease （RDD）. Methods The MR findings of 4 patients with intracranial Rosai-Dorfman Ddisease were retrospectively reviewed. .All cases were proved by pathology. Related Chinese medical literature were reviewed. Results 2 cases presented as dural mass, iso signal intensity on T1WI and iso-hypo signal intensity on T2WI,.homogeneous enhancement with dural tail..1 case involved both dural and leptomeninges..1 case diffusely involved cranial base,.cavernous sinus and nasal sinuses. Conclusion Intracranial RDD can be divided into 5 types, dural type,.dural＋leptomeningeal type,.brain parenchymal type,.sella turcica type and ventricle type..Dural type is the most common type..The center of lesion shows lower signal intensity on T2WI than the peripheral area may be the MRI characteristic of intracranial RDD.

关 键 词：组织细胞增多症 窦 中枢神经系统 磁共振成像 

分 类 号：R741[医药卫生—神经病学与精神病学] R445.2[医药卫生—临床医学]