Anaemia in Waldmann's disease: A rare presentation of a rare disease  

作　　者：Shahira A El-Etreby Ahmed Y Altonbary Mohamed El Sorogy Wagdi Elkashef Jehan A Mazroa Monir H Bahgat 

机构地区：[1]Divisions of Hepatology and Gastroenterology, Pathology, and Diagnostic Radiology, Specialized Medical Hospital and Gastrointestinal Surgery Center

出　　处：《World Journal of Gastrointestinal Endoscopy》2015年第5期567-572,共6页世界胃肠内镜杂志（英文版）（电子版）

基　　金：Supported by Specialized Medical Hospital and Gastrointestinal Surgery Center,Mansoura University,Mansoura,Egypt

摘　　要：A 32-year-old female presented with 5-year history of iron deficiency anemia, marked pallor and edema of both lower limbs. Laboratory investigations including complete blood count, blood film, iron studies, lipid profile, ascitic fluid analysis, test of stool for occult blood and alpha 1 anti-trypsin. Upper, lower gastrointestinal(GIT) endoscopies, and enteroscopy were performed. Imaging techniques as abdominal ultrasonography and computed tomography were done. Echocardiography, lymph node biopsy and bone marrow examination were normal. The case was diagnosed as Waldmann's disease with protein losing enteropathy and recurrent GIT bleeding. Management started with low fat diet with medium chain triglyceride, octreotide 200 μg twice a day, tranexamic acid and blood transfusion. Then, exploratory laparotomy with pathological examination of resected segment was done when recurrent GIT bleeding occurred and to excluded malignant transformation.A 32-year-old female presented with 5-year history ofiron deficiency anemia, marked pallor and edema ofboth lower limbs. Laboratory investigations includingcomplete blood count, blood film, iron studies, lipidprofile, ascitic fluid analysis, test of stool for occult bloodand alpha 1 anti-trypsin. Upper, lower gastrointestinal（GIT） endoscopies, and enteroscopy were performed.Imaging techniques as abdominal ultrasonography andcomputed tomography were done. Echocardiography,lymph node biopsy and bone marrow examinationwere normal. The case was diagnosed as Waldmann＇s disease with protein losing enteropathy and recurrentGIT bleeding. Management started with low fat diet withmedium chain triglyceride, octreotide 200 μg twice a day,tranexamic acid and blood transfusion. Then, exploratorylaparotomy with pathological examination of resectedsegment was done when recurrent GIT bleeding occurredand to excluded malignant transformation.

关 键 词：Waldmann's disease LYMPHANGIECTASIA GASTROINTESTINAL BLEEDING Iron DEFICIENCY ANEMIA 

分 类 号：R556[医药卫生—血液循环系统疾病]