先天性多发性靶样含铁血黄素沉积性血管瘤1例  

A Case of Congenital Multiple Targetoid Hemosiderotic Hemangioma

作　　者：曹畅[1] 解瑶[1] 华薇[1] 李利[1] 

机构地区：[1]四川大学华西医院,四川成都610041

出　　处：《中国皮肤性病学杂志》2015年第10期1057-1058,1061,共3页The Chinese Journal of Dermatovenereology

摘　　要：患儿女,8岁。全身紫红色斑疹、丘疹、斑块8年。全身可见散在分布绿豆至钱币大紫红色斑疹、丘疹、斑块、褐色色素沉着斑及白色萎缩性色素减退斑。腹部丘疹样皮损病理示真皮乳头层及浅中层大量增生扩张的薄壁血管腔样结构,部分可见胞核稍突出,胞浆少的鞋钉样内皮细胞凸向管腔。免疫组化示淋巴管内皮细胞标志(D2-40)阳性,Wilms Tumor-1(WT-1)阴性。诊断:先天性多发性靶样含铁血黄素沉积性血管瘤。An eight - years - old girl presented with violaceous maculas, papules and plaques on the whole body for eight years. Her body was scattered with different size of violaceous maculas, papules, plaques, brown pig- mentations and white atrophic hypopigmentations. Histopathology： proliferation of dilated thin walled mature vascular structures within the superficial dermis. The endothelial lining with hobnailing of nuclei protruding into the channel space. Endothelial lining with positive immunohistochemical stain for D2-40 but negative for Wiims tumor-1. She was diagnosed as congenital multiple targetoid hemosiderotic hemangioma.

关 键 词：靶样含铁血黄色沉积性血管瘤 先天性 多发性 

分 类 号：R739.5[医药卫生—肿瘤]