原发性胆汁性肝硬化合并肺间质病变1例  

One case of primary biliary cirrhosis with pulmonary interstitial lesions

作　　者：龙历 吴亚云[1] 

机构地区：[1]贵州医科大学感染病学教研室,贵州省贵阳市550004

出　　处：《世界华人消化杂志》2016年第12期1938-1942,共5页World Chinese Journal of Digestology

摘　　要：原发性胆汁性肝硬化(primary biliary cirrhosis,PBC)在疾病的进展过程中,可累及肺部,特别是炎症活动的PBC患者更易出现肺间质病变,其临床表现及影像学改变与普通肺炎相似,抗生素治疗无效.回顾性分析贵州医科大学附属医院1例PBC合并肺间质病变患者的临床资料,并复习相关文献.研究表明,PBC合并肺间质病变的临床表现缺乏特异性,易误诊为社区获得性肺炎,及时免疫抑制剂治疗有效.To improve the understanding of primary biliary cirrhosis complicated with interstitial lung disease,we retrospectively analyzed theclinical information of one patient who had primary biliary cirrhosis complicated with interstitial lung disease,and reviewed the related literature.Primary biliary cirrhosis could affect the lung in the disease progression and result in pulmonary interstitial disease,especially in PBC with infl ammatory activity.It is similar to common pneumonia in clinical manifestations and imaging appearances,and antibiotic treatment is ineffective.Primary biliary cirrhosis with clinical manifestations of interstitial lung disease lacks specifi city and is easily misdiagnosed as community-acquired pneumonia,but timely immunosuppressant therapy is effective.

关 键 词：原发性胆汁性肝硬化 肺间质病变 肺部感染 

分 类 号：R575.2[医药卫生—消化系统]