四肢腺泡状软组织肉瘤MRI诊断  

MRI Diagnosis of Alveolar Soft part Sarcoma

作　　者：李彩霞[1] 徐焱[1] 赵福香[1] LI Caixia XU Yan ZHAO Fuxiang(Jiaozuo No. 2 Hospital,Jiaozuo, Henan Province 454001, P. R. China)

机构地区：[1]河南省焦作市第二人民医院磁共振室,454001

出　　处：《临床放射学杂志》2016年第11期1730-1734,共5页Journal of Clinical Radiology

摘　　要：目的探讨腺泡状软组织肉瘤(ASPS)的MRI表现特征。方法搜集经手术、病理证实的6例ASPS患者的影像学资料,分析其MRI表现。结果女5例,男1例,中位年龄(17.67±2.63)岁。肿瘤发生位置:上肢1例,大腿4例,小腿1例。MRI显示肿瘤体积较大,边界清晰,肿瘤实质内、肿瘤边缘或周围可见大量蜿蜒迂曲的流空血管。T1WI和T2WI均为高信号,增强后明显强化。病理显示大量多边形肿瘤细胞围成肿瘤巢,呈腺泡样排列,PAS染色阳性,CD34染色显示细胞巢之间的血窦内皮细胞阳性。结论 ASPS为富血供恶性肿瘤,其临床、MRI及病理表现具有一定特征性。Objective To investigate the characteristics of MRI manifestation of alveolar soft part sarcoma （ASPS）. Methods The radiographic data of 6 cases with ASPS proven by surgery and biopsy were collected in the study and the MRI appearances were analyzed retrospectively. Results 5 females and 1 male were selected into this group. The median age was 17.67 ±2.63 years old. One tumor was located in upper limb,four in the thighs,and one was located in the legs. MR demonstrated the tumors had a large diameter and a well-defined margin. Tumors were hyperintense on T2-weighted and Tf-weighted images with many flow voids and persistent remarkable enhancement. Pathological examination revealed solid nests of several polygonal tumor cells arranged in an alveolar pattern and separated by thin walls. Tumor cells were noted on periodic acid-Schiff（PAS）stains. The endothelial cells of sinusoidal vascular channels were positive on CD34. Conclusion ASPS is a kind of rare malignancy with a rich blood supply, and there were some characteristics about its clinical and MRI features to some degree.

关 键 词：磁共振成像 肉瘤 软组织腺泡状 

分 类 号：R738.7[医药卫生—肿瘤] R445.2[医药卫生—临床医学]