CREST综合征合并良性自发性气腹症1例报道  

Benign spontaneous pneumoperitoneum combined with CREST syndrome:one case report

作　　者：徐蕙[1] 费贵军[2] 李骥[2] 舒慧君[2] 李景南[2] 方秀才[2] 钱家鸣[2] 

机构地区：[1]中国医学科学院北京协和医学院北京协和医院消化内科,北京100730 [2]中国医学科学院北京协和医学院北京协和医院内科,北京100730

出　　处：《胃肠病学和肝病学杂志》2016年第12期1338-1340,共3页Chinese Journal of Gastroenterology and Hepatology

摘　　要：系统性硬化包括CREST[钙质沉积(calcinosis cutis)、雷诺现象(Raynaud phenomenon)、食管运动功能障碍(esophageal dysmotility)、指端硬化(sclerodactyly)、毛细血管扩张(telangiectasia)]综合征,常可累及消化系统,几乎整个胃肠道均可受累,其中以胃食管反流最多见,假性肠梗阻是较为少见的一种合并症,而合并自发性气腹症者,至今国内未见报道。现报道1例我院收治的CREST综合征合并良性自发性气腹症患者,供临床医师参考。The gastrointestinal tract is commonly involved in patients with systemic sclerosis （SSc） including CREST syndrome （calcinosis, Raynaud phenomenon, esophageal dysmotility, sclerodactyly, telangiectasia）. Virtually all parts of the gastrointestinal tract can be involved, although the esophagus is the most frequently reported. Pseudo-obstruction is less common, while benign spontaneous pneumoperitoneum is a rare complication of SSc, which has never been repor- ted in China till now. Here, one case of benign spontaneous pneumoperitoneum combined with CREST syndrome was re- ported.

关 键 词：系统性硬化 CREST综合征 良性自发性气腹症 肠气囊肿病 

分 类 号：R574.2[医药卫生—消化系统]