家族性渗出性玻璃体视网膜病变临床研究  

Clinical study of familial exudative vitreoretinopathy

作　　者：苏满想[1] 张国明[2] 李战[1] 薛艳[1] 张天测[1] 王培锋[1] 赵如焕[1] 曾少花 付琴[1] 

机构地区：[1]广东省珠海市妇幼保健院眼科,519001 [2]深圳市眼科医院

出　　处：《中国斜视与小儿眼科杂志》2016年第4期23-24,I0001-I0002,共4页Chinese Journal of Strabismus & Pediatric Ophthalmology

摘　　要：目的观察新生儿时期的家族性渗出性玻璃体视网膜病变(Familial Exudative Vitreoretinopathy,FEVR)的发病状况及临床特征。方法回顾性分析于2014年1月至2016年3月在我院行Retcam眼底筛查中被临床诊断为FEVR的103例169眼的临床资料。结果 16446例新生儿中发现FEVR病变103例,发生率为0.63%。其中有3例(2.91%)是早产或低出生体重儿。103例169眼中,1期156眼(92.31),2期9眼(5.33%),4期4眼(2.36%),3期及5期均未见(0%)。大多数(92.31%)患者病情好转或趋于稳定,随访观察,需要激光治疗的5例9眼,占5.33%。结论(1)FEVR和早产儿视网膜病变的临床特征非常相似,其鉴别诊断需进一步完善。(2)大部分患儿属于FEVR的早期,暂不需治疗,但也有部分需要尽快进一步治疗,挽救患儿视力。Objective To observe the clinical features and incidence of familial exudative vitreoretinopathy（FEVR）.Methods A retrospective analysis was conducted on 103 newborns who diagnosed as FEVR by RetCam from January 2014 to March 2016.Results Among the 16446 newborns 103 cases（0.63%）developed FEVR.including 3 premature infants.Among the 169 eyes（103 cases） include 156 eyes（92.31%） suffering from stage 1,9 eyes（5.33%） from stage 2,4eyes（2.36%） from stage 4,0 eye from stage 3 and 5.Follow-up examinations were performed at most of the patients whose condition improved or be stable.5 cases need laser treatment Conclusions Clinical presentation of FEVR is similar to ROP.The differential diagnosis needs to be further improved Most of patients with early lesion don＇t require surgery.But afew patients need surgery to save sight

关 键 词：家族性渗出性玻璃体视网膜病变 新生儿 儿童广角数码眼底照相机 

分 类 号：R774.1[医药卫生—眼科]