成人双侧眼睑巨大黄色瘤一例  

Bilateral xanthogranulomas in an adult:one case report and literature review

作　　者：齐心竹 陈晗[1] 范斌[1] 李光宇[1] 

机构地区：[1]吉林大学第二医院,长春130041

出　　处：《新医学》2017年第3期197-200,共4页Journal of New Medicine

摘　　要：黄色肉芽肿性疾病(又称黄色瘤)是一种罕见的疾病,相关了解甚少,由于含有脂类的细胞在真皮或皮下组织内聚集,可在皮肤表面形成黄色的瘤状损害。黄色瘤常可划分为4个临床亚型:成人型黄色肉芽肿、成人哮喘眼周型黄色肉芽肿、坏死型黄色肉芽肿与脂质型黄色肉芽肿型。主要区别在他们的临床特征,组织病理学和各系统功能,然而有时这些条件之间存在重叠。该文报告1例双侧眼睑和眼眶巨大黄色肉芽肿性疾病,最后诊断为黄色瘤患者。Xanthogranuloma is a rare and poorly understood disorder,manifested with the accumulation of cells containing lipid in the dermis or subcutaneous tissues,which can form yellow tumor-like lesions on the cutaneous surface.Xanthogranuloma can be classified into four clinical subtypes：adult-onset xanthogranuloma,adult-onset asthma and periocular xanthogranuloma,necrotic xanthogranuloma and Erdheim-Chester disease.These subtypes primarily differ in terms of clinical features,histopathology and systemic functions,although these conditions overlap occasionally.We reported one case of xanthogranuloma presenting with xanthomatous masses in bilateral eyelids and orbits.

关 键 词：眼睑 黄色肉芽肿 杜顿细胞 

分 类 号：R739.71[医药卫生—肿瘤]