小肠原发性粒细胞肉瘤1例并文献复习  

Primary granulocytic sarcoma of small intestine:a case report and literature review

作　　者：章俏雷[1] 方炳木[1] 曲志刚[1] 刘永华[1] 江锦红[1] 马光丽[1] 

机构地区：[1]温州医科大学附属第六医院,浙江省丽水市人民医院血液科,浙江丽水323000

出　　处：《临床血液学杂志》2017年第2期228-230,共3页Journal of Clinical Hematology

基　　金：浙江省科技厅项目(No:2012C33110)

摘　　要：原发性粒细胞肉瘤（primary granulocytic sarcoma,PGS）是指幼稚粒细胞在骨髓外的组织增殖所形成的髓系恶性肿瘤,由于不伴有血液系统的异常,其误诊率高;若不早期诊断和治疗,疾病进展快,多会发展为急性白血病,预后极差;及早正确的诊断与强有力的化疗对患者的远期生存十分重要，To study the diagnosis of primary granulocytic sarcoma of small intestine （PGS） and put forward the new treatment of the disease. A case of PGS was reported and the related literatures of PGS in recent 10 years were reviewed. Nine cases presented clinically with abdominal pain, the diagnosis was based on the immunohisto-chemistry,and combination chemotherapy was the main treatment. Immunohistochemistry is extremely important for the diagnosis of PGS,the prognosis of PGS is poor, and the intensive chemotherapy is associated with longer survival.

关 键 词：粒细胞肉瘤 小肠 原发性 治疗 

分 类 号：R733.3[医药卫生—肿瘤]