Poland综合征诊疗的研究进展  

Progress of Diagnosis and Treatment for Poland Syndrome

作　　者：欧阳熠烨 刘春军[1] 

机构地区：[1]中国医学科学院北京协和医学院整形外科医院,北京市100144

出　　处：《组织工程与重建外科杂志》2017年第4期220-223,237,共5页Journal of Tissue Engineering and Reconstructive Surgery

基　　金：协和青年基金(3332015156);首都卫生发展科研专项基金(2016-2-4-41)

摘　　要：Poland综合征是一种罕见的胸壁组织缺损畸形,可同时伴有躯干、四肢等部位的异常。由于发病率低,其病因尚无定论,存在多种学说。而多系统、多部位的临床表现使其全面诊断较为困难,一些严重并发疾病的存在还会影响治疗时机及策略的选择。目前,Poland综合征的诊疗往往由胸外科、手外科、整形外科单独完成,缺乏系统性的病情分型、严重度评分及治疗策略。本文从病因、临床表现、治疗策略三个方面,综述Poland综合征诊疗的最新研究进展,同时对其未来发展进行展望。Poland syndrome is a rare deformity of the chest wall accompanied with the abnormality of the trunk, limbs and other parts. As the incidence is low, the uniform etiology is not yet settled, but there are various theories of it. The multi-system and multi-site clinical manifestations make it more difficult to diagnose it overall, and the presence of some serious complications will also affect the timing of treatment and strategy choice. At present, the diagnosis and treatment of Poland syndrome is often done by thoracic surgery, hand surgery, plastic surgery separately and lack systematic classification, severity score system and treatment strategies. In this paper, the latest progress of the diagnosis and treatment of Poland syndrome were introduced in detail from the aspects of etiology, clinical manifestation and treatment strategy. At the same time, the future development of diagnosis and treatment for Poland syndrome was prospected.

关 键 词：P01and综合征 乳房缺失 手畸形 上肢畸形 乳房整形术 人体可视项目 三维打印 

分 类 号：R622[医药卫生—整形外科]