成人心脏乳头状弹力纤维瘤的临床和超声心动图特征  

Clinical and echocardiographic characteristics of cardiac papillary fibroelastoma in adults

作　　者：韩建成[1] 滕飞[2] 杨旭[1] 孙琳[1] 谷孝艳[1] 张烨[1] 赵映[1] 高爽[1] 何怡华[1] HAN Jiancheng TENG Fei YANG Xu SUN Lin GU Xiaoyan ZHANG Ye ZHAO Ying GAO Shuang HE Yihua(Department of Ultrasound Department of Pathology, Beijing Anzhen Hospital, Capital Medical University, Beijing 100029, China)

机构地区：[1]首都医科大学附属北京安贞医院超声科,北京100029 [2]首都医科大学附属北京安贞医院病理科,北京100029

出　　处：《中国医学影像技术》2017年第10期1497-1500,共4页Chinese Journal of Medical Imaging Technology

基　　金：首都医学发展专项青年基金(首发2014-4-2064);心血管疾病精准医学北京实验室(116211);胎儿心脏病母胎医学北京市重点实验室(BZ0308)

摘　　要：目的探讨心脏乳头状弹力纤维瘤(CPF)的临床和超声心动图表现。方法回顾性分析经手术病理证实的13例CPF患者的临床表现、超声心动图特征、手术方式及预后。结果 13例患者临床表现不具特异性,为不同程度胸闷、气短等症状。所有肿瘤均为单发,位于瓣膜9例(9/13,69.23%),其中主动脉瓣4例、二尖瓣3例、三尖瓣2例;位于心腔4例(4/13,30.77%),其中右心房2例、右心室1例、左心室1例。肿瘤最大径>2mm者8例,最大径≤2mm者5例。超声检出8例,未检出5例。8例接受肿瘤切除,5例接受瓣膜置换术。结论 CPF临床表现不特异,当肿瘤体积较小时,超声心动图常无法发现;心脏瓣膜为其常见部位,尤其是主动脉瓣。CPF预后良好。Objective To explore the clinical features and echocardiographic characteristics of cardiac papillary fibroelas- toma （CPF） in adults. Methods Clinical features, eehocardiographic characteristics, surgical procedures and outcomes were retrospectively evaluated in 13 patients with CPF confirmed by pathology. Results The clinical features of CPF were atypical. The most common symptoms were chest distress and short breath. All the 13 patients were single lesions, 9 cases （9/13, 69. 23%） involved the valves （4 on the aortic valve, 3 on the mitral valve, 2 on the tricuspid valve） and 4 cases （4/ 13, 30.77%） involved the chambers （2 in the right atrium, 1 in the right ventricle, 1 in the left ventricle）. The largest di- ameters of 〉2 mm were in 8 cases and ≤2 mm were in 5 cases. Eight cases were detected by echocardiographic examina- tion and 5 cases were missed. Surgical excision was performed in 8 patients and prosthetic valve replacement was performed in 5 patients. Conclusion The clinical symptoms of CPF are variable. When the size of CPF is too small, eehoeardiography is difficult to detect. Most of CPFs originate on the valves, predominantly on the aortic valve. The prognosis of CPF is excellent.

关 键 词：心脏肿瘤 乳头状弹力纤维瘤 超声心动描记术 

分 类 号：R732.1[医药卫生—肿瘤] R540.45[医药卫生—临床医学]