腹内型侵袭性纤维瘤病的诊治分析(附8例报道)  

Diagnosis and treatment of intra-abdominal aggressive fibromatosis: a report of 8 cases

作　　者：任项项 田雨[1] 肖刚[1] 张萌[2] 

机构地区：[1]中国医科大学附属盛京医院普外科,沈阳110004 [2]中国医科大学附属第一医院皮肤科,沈阳110004

出　　处：《中国普外基础与临床杂志》2017年第11期1361-1364,共4页Chinese Journal of Bases and Clinics In General Surgery

摘　　要：目的总结腹内型他爱侵袭性纤维瘤病的临床特点和治疗力方法。方法回顾性分析中国医科大学附属盛京医院普外科于2011年2月至2017年3月期间收治的8例经女病理学检查证实的腹内型侵袭一性纤维瘤病患者的临床病理学资料。结果 8例患者中.男3例,女5例;临床表现为单纯腹痛4例(反复间断性腹痛2例,急性腹痛2例),腹部包块3例,外院术后复发1例(余7例系初次就诊);病程为4~720d,中位数为130d,所有患者行根治性手术,手术时间为92-493 min,平均246 min;术中出血量为20~1000mL,平均321mL;全部病例术中放置腹腔引流管,引流管放置时间为5~9d,平均6d;住院时间为11~75d,平均25d:术后2例患并者出现腹痛症状,术后8例患者均获访,随访时间为6~40个月,中位数为23个月,1例患者于术后212 d复发,其余7例患者随访期间无复发。结论腹内墦侵徙袭性纤维瘤病的术前明确诊断较术闲难,出现临床症状时首选手术治疗。Objective The aim of this article is to analyze the clinical characteristics of intra-abdominal aggressive fibromatosis and discuss its treatment methods. Methods Retrospective analysis of the clinical data in 8 cases of intra-abdominal aggressive fibromatosis who were confirmed by surgery and pathological diagnosis between Feb. 2011 and Mar. 2017 in Shengjing hospital was performed. Results Of the 8 cases （3 males and 5 females）, there were 4 cases of simple abdominal pain （2 cases of repeated intermittent abdominal pain and 2 cases of acute abdominal pain）, 3 cases of abdominal mass, and 1 case of relapses after surgery in outside hospital （others 7 cases were the first visit）. The course of disease was 4 to 720 d, with median of 130 d. All cases underwent radical surgery, and the operative time was 92 to 493 min, with an average of 246 rain. Intraoperative blood loss was 20 to 1 000 mL, with an average of 321 mL. The drainage tube placement time in all patients was 5 to 9 d, with an average of 6 d. The hospital stay was 11 to 75 d, with an average of 25 d. Two cases suffered from postoperatively appeared abdominal pain symptoms. All cases were followed-up for 6 to 40 months, with median of 23 months. During the follow-up period, 1 case relapsed on 212 d after surgery, and the remaining 7 cases had no recurrence. Conclusion For intra-abdominal aggressive fibromatosis, it is difficult to make clear diagnosis before operation and surgery is the primary choice of treatment when symptom appeared.

关 键 词：腹内型侵袭性纤维瘤病 诊断 治疗 复发 

分 类 号：R738.6[医药卫生—肿瘤]