气管腔内血管周上皮样细胞肿瘤病例报道并文献复习  

A case report of perivascular epithelioid cell tumor and literature review

作　　者：周俊 王磊[2] 丁寿来 丁惠珍 黄玉民 Zhou Jun;Wang Lei;Ding Shoulai;Ding Huizhen;Huang Yumin(Department of Respiratory Medicine, Affiliated Hospital of Yangzhou University, Yangzhou 225000, Chin)

机构地区：[1]扬州大学附属医院呼吸科,225000 [2]扬州大学附属医院病理科,225000

出　　处：《国际呼吸杂志》2018年第1期15-19,共5页International Journal of Respiration

摘　　要：【摘要】目的探讨气管腔内血管周上皮样细胞肿瘤（PEComa）的病因、临床表现、诊断、鉴别诊断、治疗及预后。方法回顾性分析扬州大学附属医院2017年3月31日收治的1例支气管腔内PEComa患者的临床资料，并复习相关文献。结果肿瘤肉眼为灰白、淡黄、实性，质地中等；免疫组织化学结果：HMB-45（＋），Melan-A（＋），S-100（＋），SMA（＋），Desmin（＋），CD34（＋），Vimentin（＋），Ki-67（1％＋）；病理诊断为PEComa。结论支气管腔PEComa罕见，经支气管镜高频电凝圈套＋氩离子凝固术治疗支气管腔PEComa是一种经济、创伤小的治疗方法。Objective To investigate the etiology, clinical manifestation, diagnosis, differential diagnosis, treatment and prognosis of perivascular epithelioid cell tumor （PEComa）. Methods The ciinical data of one patient with bronchial PEComa treated in Affiliated Hospital of Yangzhou University on March 31,2017 were analyzed, and the related literatures were reviewed. Results The pale and yellowish PEGoma with medium texture was stained positively with HMB-45, Melan-A, S-100, SMA, Desmin, CD34, Vimentin, Ki-67 （1%） by immunohistochemistry, and its pathological diagnosis was PEComa. Conclusions Bronchial PEComa is rare. The high frequency electrocoagulation snare by bronchoscope with argon plasma coagulation is an economic and less trauma method.

关 键 词：血管周上皮样细胞肿瘤 支气管镜 高频电凝圈套 

分 类 号：R734.1[医药卫生—肿瘤]