卡波西样血管内皮瘤研究进展  

Research progress of Kaposiform hemangioendothelioma

作　　者：张源方 董长宪 Zhang Yuanfang;Dong Changxian(Department of Hemangioma Surgery, Zhengzhou University People＇s Hospital, Henan Provincial People＇s Hospital, Zhengzhou 450052, Chin)

机构地区：[1]郑州大学人民医院河南省人民医院血管瘤外科,450052

出　　处：《中华实用儿科临床杂志》2018年第11期874-877,共4页Chinese Journal of Applied Clinical Pediatrics

基　　金：河南省医学科技攻关计划项目（201403152）

摘　　要：卡波西样血管内皮瘤（KHE）是一种组织形态类似于卡波西肉瘤（KS）且具有侵袭性的肿瘤，好发于婴幼儿和儿童，较罕见，多发于四肢、躯干上部、颌面部的皮肤及深部软组织，也可发生于纵隔、腹膜后等。KHE是引起婴幼儿卡梅现象（KMP）的主要肿瘤之一，病死率高达10%～37%，甚至达52%。目前国内外并无统一、有效的治疗方法，现就KHE的临床表现、诊断、治疗等进行综述。Kaposiform hemangioendothelioma（KHE） is a kind of organization form is similar to Kaposi＇s sarcoma（KS） and aggressive cancer,found in children and infants are rare and multiple in the limbs, torso, facial skin and deep soft tissue can also occur in the mediastinum,retroperitoneal etc. KHE is one of the main causes of Kasabach Meritt phenomenon（KMP） in infants and young children, the mortality rate is as high as 10% -37% , even 52%. At present,there is no uniform and effective treatment method at home and abrnad. The clinical manifestations, diagnosis and treatment of KHE are reviewed.

关 键 词：卡波西样血管内皮瘤 卡梅现象 血管瘤 血小板减少 

分 类 号：R732.2[医药卫生—肿瘤]