下丘脑神经元错构瘤研究进展  

Recent advance in hypothalamic neuronal hamartoma

作　　者：齐洪武[1] 曾维俊 Qi Hongwu;Zeng Weijun(Department of Neurosurgery,Bethune International Peace Hospital of PLA,Shijiazhuang 050082,Chin)

机构地区：[1]解放军白求恩国际和平医院神经外科,石家庄050082

出　　处：《中华神经医学杂志》2018年第7期750-754,共5页Chinese Journal of Neuromedicine

摘　　要：下丘脑神经元错构瘤（HNH）是罕见的先天脑发育异常性中枢神经系统病变，其解剖部位居于第三脑室底部、灰结节及乳头体的附近，主要由异位脑灰质、神经元、神经胶质细胞和纤维束等组成。本文就HNH的病因及病理、临床表现、临床分型、影像学特征、治疗方案等研究进展综述如下。Hypothalamic neuronal hamartomas are rarely congenital developmental neuronal masses. They often attach to the third ventricle floor, mammillary bodies and tuber cinereum, and they are composed ofheterotopic gray matter, neurons, glia and myelinated fibers. This article summarizes the etiologies, pathologies, clinical manifestations and classifications, imaging features and therapy methods of hypothalamic neuronal hamartomas.

关 键 词：下丘脑 神经元 错构瘤 痴笑性癫痫 性早熟 显微外科手术 

分 类 号：R739.41[医药卫生—肿瘤]