Sturge-Weber综合征合并浅前房高眼压一例  

A case of glaucoma with narrow angle related with Sturge-Weber syndrome

作　　者：次仁琼达 刘江 郭春英[2] 吴元[2] CI Ren-qiongda;Liu Jiang;Guo Chun-ying(Department of Ophthalmology,People＇s Hospital of Tibet Autonomous Region,Lasa 850000,China)

机构地区：[1]西藏自治区人民医院眼科,850000 [2]北京大学第一医院

出　　处：《中国斜视与小儿眼科杂志》2018年第3期38-38,I0009,I0010,共3页Chinese Journal of Strabismus & Pediatric Ophthalmology

摘　　要：Sturge-Weber综合征为一种罕见的先天性脑及颜面部血管瘤,常累及眼部引起青光眼,且均表现为宽房角型。本文报道1例Sturge-Weber综合征合并浅前房高眼压。经术中探查,发现浅前房的原因为晶体虹膜后机化膜形成,阻断了房水向前房的流动。推测病因和本病伴发的脉络膜血管瘤有关。本文首次对Sturge-Weber综合征引起的浅前房青光眼进行病例报道,希望能增加对本病眼部并发症的进一步认识。Sturge-Weber Syndrome（SWS） is a rare neuro-oculocutaneous disorder which may involve eyes and manifest as glaucoma. All the SWS patients with glaucoma have wide angles in eye balls. But this patient have a very narrow angle with high intraocular pressure. After operative exploration we found there was an exudative membrane behind and adhering to iris-lens diaphragm. The flow of aqueous humor from posterior chamber to anterior chamber was blocked and it was the reason of high IOP. We suspect the membrane be correlated with choroidal hemangiomas which is another ocular component of SWS. It is first time we have such a case of second glaucoma with narrow angle induced by SWS. We hope this case can help us to understand SWS deeply.

关 键 词：STURGE-WEBER综合征 青光眼 脉络膜血管瘤 窄房角 高眼压 

分 类 号：R775[医药卫生—眼科] R739.4[医药卫生—临床医学]