肝脏型恶性神经纤维瘤病(附二例报告)  

Hepatic Malignant Neurofibromatosis(Report of 2 Cases)

作　　者：和毓天[1] 李常茂[1] 阎东[1] 范承经[1] 袁曙光[1] 孙勇[1] 李伟[1] 黎冠群[2] 危群[2] 白中华[3] 施德明[4] 

机构地区：[1]昆明医学院第二附属医院放射科 [2]昆明医学院第二附属医院病理科 [3]昆明医学院第二附属医院检验科 [4]昆明医学院第二附属医院功能科

出　　处：《临床放射学杂志》1991年第5期235-237,T035,共4页Journal of Clinical Radiology

摘　　要：本文报告2例罕见的以肝脏病损为主的恶性神经纤维瘤病。本病主要应与原发性肝细胞癌(HCC)或肝内转移瘤鉴别。临床经过缓慢.临床检验提示肝脏恶性病变可能而不支持HCC.肝动脉造影结节内部显影浅淡,外周浓密;对碘化油显示敏感性低,且吸收块。病理确诊之前,全误诊。Two rare cases of malignant neu-rofibromatosis with principle lesion inthe liver are reported.The main dif-ferential diagnosis was made witch theprimary hepatoma or the intrahepaticmetastatic carcinoma.The clinical co-urse developed gradually.Laboratoryexaminations suggested a possibilityof malignant hepatic lesion,but notagree with hepatocellular carcinoma.Hepatic angiography showed noduleswith a much minor opacity in its cen-tral area than its periphery.Only asmall amount of iodized oil stayed fora short time in the nodules.All thetwo cases were misdiagnosed beforepathological examination.The mecha-nism of some X-ray signs is discussed.

关 键 词：神经纤维瘤 肝 血管造影 

分 类 号：R739.404[医药卫生—肿瘤]