特发性门脉高压研究现状  

Progress of idiopathic portal hypertension

作　　者：任艳 郑素军 REN Yan;ZHENG Sujun(Complicated Liver Diseases and Artificial Liver Treatment & Training Center,Beijing YouAn Hospital,Capital Medical University,Beijing 100069,China)

机构地区：[1]首都医科大学附属北京佑安医院疑难肝病及人工肝中心

出　　处：《胃肠病学和肝病学杂志》2019年第6期708-710,共3页Chinese Journal of Gastroenterology and Hepatology

基　　金：国家科技重大专项“艾滋病和病毒性肝炎等重大传染病防治”(2017ZX10302201-004,2017ZX10202203-006)

摘　　要：特发性门脉高压(idiopathic portal hypertension, IPH)临床少见,目前对于该疾病的命名尚缺乏统一的标准。临床表现为门脉高压但无肝硬化的存在。对于该病的发病机制目前未完全清楚。因缺乏特异的检测指标,所以临床诊断较困难。该病的病理表现多样,肝脏活组织检查能除外肝硬化及其他原因引起的门脉高压,进而协助该病的诊断。治疗方面主要是针对门脉高压引发的并发症的治疗和预防。Idiopathic portal hypertension (IPH) is rare and the current name for the disease is still a lack of uniform standards. The clinical manifestations are portal hypertension without liver cirrhosis. The pathogenesis is not completely clear. Due to the lack of specific markers, clinical diagnosis is difficult. The pathologic manifestations of the disease are diverse and liver biopsy can help diagnose the disease by excluding portal hypertension caused by cirrhosis and other reasons. Treatment is mainly for the management and prevention of complications caused by portal hypertension.

关 键 词：门脉高压 特发性 结节性再生性增生 

分 类 号：R575.2[医药卫生—消化系统]