Persistent fifth aortic arch stenosis associated with type A interruption of the aortic arch: a report of six cases  

作　　者：Lin Zheng Yong-Li Cao Rong-Chang Wu Jian Guo Ning Ma Fang-Yun Wang Xin Zhang Yun Peng 

机构地区：[1]Department of Echocardiography,Beijing Children's Hospital,Capital Medical University,National Center for Children's Health,Beijing 100045,China [2]Department of Radiology,Beijing Children's Hospital,Capital Medical University,National Center for Children's Health,Beijing 100045,China [3]Department of Cardiac Surgery,Beijing Children's Hospital,Capital Medical University,National Center for Children's Health,Beijing 100045,China

出　　处：《Chinese Medical Journal》2019年第12期1482-1484,共3页中华医学杂志（英文版）

摘　　要：Persistent fifth aortic arch (PFAA) is a rare congenital cardiovascular malformation that occurs when the pharyngeal fifth aortic arch does not degenerate during the embryonic period. The first case of PFAA was described in an autopsy specimen in 1969.[1] In 1973, the persistence of a left fifth aortic arch was first reported.[2] Since then, several case reports have described PFAA in different forms. PFAA stenosis associated with type A interruption of the aortic arch (type-A IAA) is most common in clinical practice and requires surgical intervention. From 2013 to 2018, six cases [Table 1 and Table 2] were diagnosed using echocardiography and computed tomography angiography (CTA). Five cases were successfully treated with surgery and followed-up. The purpose of this study was to summarize the clinical characteristics and diagnostic features of PFAA stenosis associated with type-A IAA to improve its diagnostic accuracy and allow for complete pre-operative preparation and proper treatment.

关 键 词：PERSISTENT FIFTH aortic arch STENOSIS type A INTERRUPTION SIX CASES 

分 类 号：R[医药卫生]