中国慢性炎性脱髓鞘性多发性神经根神经病诊治指南2019  被引量:35

Chinese guidelines for diagnosis and treatment of chronic inflammatory demyelinating polyradiculoneuropathy 2019

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作  者: 卢家红 蒲传强[6] 崔丽英[7] 林洁[8] 无;Lu Jiahong;Pu Chuanqiang;Cui Liying(Chinese Society of Neurology;Peripheral Neuropathy Collaboration Group of Chinese Society of Neurology;Chinese Society of Electromyography and Clinical Neuroelectrophysiology;Chinese Society of Neuromuscular Disease;Department of Neurology,Huashan Hospital,Fudan University,Shanghai 200040,China;Department of Neurology,People's Liberation An.i,y General Hospital,Beijing 100853,China;Department of Neurology,Peking Union Medical College Hospital,Chinese Academy of Medical Sciences,Beijing 100730,China)

机构地区:[1]中华医学会神经病学分会 [2]中华医学会神经病学分会周围神经病协作组 [3]中华医学会神经病学分会肌电图与临床神经电生理学组 [4]中华医学会神经病学分会神经肌肉病学组 [5]复旦大学附属华山医院神经内科,上海200040 [6]解放军总医院神经内科,北京100853 [7]中国医学科学院北京协和医院神经科,100730 [8]复旦大学附属华山医院

出  处:《中华神经科杂志》2019年第11期883-888,共6页Chinese Journal of Neurology

摘  要:近年,慢性炎性脱髓鞘性多发性神经根神经病(CIDP)在诊断、抗体发现和治疗方面都有长足进展,尤其是新型抗体介导的CIDP在治疗上有一定的特殊性。因此,在2012版基础上,更新了经典型、变异型及新型抗体介导的CIDP的定义,提出了CIDP临床和电生理诊断标准、鉴别诊断和治疗。本指南旨在为临床神经科医生提供CIDP诊断和治疗依据。There are progresses in diagnose,novel anti-bodies and treatment of chronic inflammatory demyelinating polyradiculoneuropathy(CIDP)in recent years.The treatment of paranodal anti-bodies mediated CIDP is specific.Based on the guideline of CIDP in China in 2012,this guideline revised the definitions of typical,untypical and IgG4 antibodies mediated CIDP.Moreover,the clinical and electrodiagnostic criteria as well as treatment of CIDP are published.This guideline aims to provide the diagnosis criteria and treatment of CIDP to clinical neurologists.

关 键 词:多发性神经根性神经病 慢性感染性脱髓鞘性 诊断 治疗学 指南 

分 类 号:R74[医药卫生—神经病学与精神病学]

 

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