儿童预激性心肌病4例并文献复习  

Preexcitation cardiomyopathy in children:four cases report and literature review

作　　者：董旭情 冯琳[1] 王晓宁[1] 吴新华[1] 何娟 Dong Xuqing;Feng Lin;Wang Xiaoning;Wu Xinhua;He Juan(Department of Pediatrics,the Second Hospital of Hebei Medical University,Shijiazhuang 050000,China)

机构地区：[1]河北医科大学第二医院儿科,河北石家庄050000

出　　处：《临床荟萃》2020年第11期1015-1018,共4页Clinical Focus

摘　　要：目的分析4例预激性心肌病患儿的临床特点、治疗及随访,了解该病转归,同时探讨该病的影响因素。方法回顾性分析我院4例预激性心肌病患儿临床资料,并复习文献,了解该病转归及影响因素。结果4例患儿均符合预激性心肌病诊断标准。其中3例行心内电生理学检查,发现存在旁道,给予射频消融术,病例1和病例2预激综合征消失,病例3仍有预激综合征;复查心脏超声示左心室均逐渐回缩,左心室功能均较前明显好转;此病预后良好。病例4尚未行射频消融术,目前正在随访中。结论射频消融术为预激性心肌病首选治疗方法,预后良好。诊断时年龄、预激的负荷(持续性或间歇性)及预激的类型(旁道位置及数量)是预激性心肌病的影响因素。Objective To analyze the clinical features,treatment and follow-up of 4 children with preexcitation cardiomyopathy,to understand the prognosis of the disease and to explore the influencing factors of preexcitation cardiomyopathy.Methods The clinical data of 4 children with preexcitation cardiomyopathy in our hospital were analyzed retrospectively,and the literature were reviewed to understand the prognosis and influencing factors of the disease.Results All the 4 children met the diagnostic criteria of preexcitation cardiomyopathy.Totally 3 cases of them underwent intracardiac electrophysiological examination and were found with accessory pathways,then radiofrequency ablation was performed.The preexcitation syndrome of case 1 and case 2 disappeared,while case 3 still had such syndrome.Echocardiography showed that the left ventricle gradually retracted and its function was significantly improved.The prognosis of the disease was favorable.Case 4 had not yet undergone radiofrequency ablation and was currently at follow-up.Conclusion The radiofrequency ablation is the first choice for the treatment of preexcitation cardiomyopathy and the prognosis is favorable.Age at diagnosis,preexcitation load(persistent or intermittent)and type of preexcitation(location and number of accessory pathways)are the influencing factors of preexcitation cardiomyopathy.

关 键 词：预激综合征 导管消融术 旁道 不同步 

分 类 号：R741.77[医药卫生—神经病学与精神病学]