Budd-Chiari syndrome associated with liver cirrhosis: A case report  

作　　者：Qiao-Bo Ye Qin-Feng Huang Yao-Chang Luo Yi-Lei Wen Zi-Kun Chen Ai-Ling Wei 

机构地区：[1]Basic Medical College,Chengdu University of Traditional Chinese Medicine,Chengdu 611137,Sichuan Province,China [2]Department of Oncology,The First Affiliated Hospital,Guangxi University of Chinese Medicine,Nanning 530023,Guangxi Zhuang Autonomous Region,China [3]Department of Intervention,The First Affiliated Hospital,Guangxi University of Chinese Medicine,Nanning 530023,Guangxi Zhuang Autonomous Region,China [4]Department of Pathology,The First Affiliated Hospital,Guangxi University of Chinese Medicine,Nanning 530023,Guangxi Zhuang Autonomous Region,China [5]Graduate School,Guangxi University of Chinese Medicine,Nanning 530200,Guangxi Zhuang Autonomous Region,China [6]Department of Liver Disease,The First Affiliated Hospital,Guangxi University of Chinese Medicine,Nanning 530023,Guangxi Zhuang Autonomous Region,China

出　　处：《World Journal of Clinical Cases》2021年第12期2937-2943,共7页世界临床病例杂志

基　　金：National Natural Science Foundation of China,No.81760851;Doctoral Research Start-up Fund of Guangxi University of Chinese Medicine,No.2019BS035.

摘　　要：BACKGROUND Budd-Chiari syndrome(BCS)is a rare heterogeneous liver disease characterized by obstruction of the hepatic venous outflow tract.The incidence of BCS is so low that it is difficult to detect in general practice and difficult to include within the scope of routine diagnosis.The clinical manifestations of BCS are not specific;hence,BCS tends to be misdiagnosed.CASE SUMMARY We report the case of a 33-year-old Chinese woman who presented with progressive distension in the upper abdomen.She was initially misdiagnosed with liver cirrhosis(LC)due to abnormalities on an upper abdominal computed tomography scan.Although she was taking standard anti-cirrhosis therapy,her symptoms did not improve.Magnetic resonance imaging showed caudate lobe hypertrophy;and dilated lumbar and hemiazygos veins.Venography revealed membranous obstruction of the inferior vena cava owing to congenital vascular malformation.A definitive diagnosis of BCS was made.Balloon angioplasty was performed to recanalize the obstructed inferior vena cava and the patient’s symptoms were completely resolved.CONCLUSIONBCS lacks specific clinical features and can eventually lead to LC. Clinicians andradiologists must carefully differentiate BCS from LC. Correct diagnosis andtimely treatment are vital to the patient's health.

关 键 词：Budd-Chiari syndrome Liver cirrhosis VENOGRAPHY Balloon angioplasty Inferior vena cava Case report 

分 类 号：R575[医药卫生—消化系统]