Turner综合征合并马蹄肾、右侧重复肾伴UPJO、双肾囊肿一例报告  

A case of Turner syndrome with horseshoe kidney and right side duplication kidney with UPJO and double kidney cyst

作　　者：王镭播 赵长永 张中屹 宋远明 李道兵 Wang Leibo;Zhao Changyong;Zhang Zhongyi;Song Yuanming;Li Daobing(Department of Urology,Affiliated Hospital of Zunyi Medical University,Zunyi 563000,China)

机构地区：[1]遵义医科大学附属医院泌尿外科,563000

出　　处：《中华泌尿外科杂志》2021年第6期475-476,共2页Chinese Journal of Urology

摘　　要：本文报道1例46 X,i(X)(q10)Turner综合征合并马蹄肾及右侧重复肾伴肾盂输尿管连接处梗阻(UPJO)和双肾囊肿,并继发右肾结石、积水形成的女性患者。全麻下行剖腹探查+右下肾部分切除术+右下肾肾盂切开取石和肾盂成形、内引流术+峡部离断成形术。有效解除UPJO,患者临床症状缓解。术后随访3个月,恢复良好。当Turner综合征合并马蹄肾伴UPJO时,开放式肾盂成形术伴峡部离断和肾固定术仍是经典的术式。This paper reports a rare clinical case of 46 X,i(X)(q10)TS in a female patient with horseshoe kidney and right duplication kidney with renal pelvic and ureteral junction stenosis and double kidney cysts,secondary to right renal calculi and hydronephrosis.After open surgical treatment,the curative effect was definite,which effectively relieved the stenosis at the junction of the renal pelvis and ureter and relieved the clinical symptoms of the patient.The patient was followed up for 3 months and recovered well.When TS is combined with horseshoe kidney with UPJO,open pyeloplasty with partial isthmus and renal fixation are still classic surgical procedures.

关 键 词：特纳综合征 马蹄肾 重复肾 肾盂输尿管连接处梗阻 

分 类 号：R699.2[医药卫生—泌尿科学]