Selection of surgical strategies for vulvar Paget’s disease  

作　　者：Yu Liu Zheng-Yong Li Ai Zhong Wijaya Wilson Adrian Jing Peng Jun-Jie Chen 

机构地区：[1]Department of Surgery,West China Hospital of Sichuan University,Chengdu,Sichuan 610041,China [2]Department of Burn and Plastic Surgery,West China Hospital of Sichuan University,Chengdu,Sichuan 610041,China

出　　处：《Chinese Medical Journal》2021年第20期2483-2485,共3页中华医学杂志（英文版）

基　　金：supported by a grant from the Sichuan Science and Technology Program(No.2020YFS0267)。

摘　　要：Extramammary Paget disease(EMPD)is an uncommon intraepithelial adenocarcinoma that tends to occur in regions with an abundance of apocrine glands.EMPD typically affects older individuals aged 50 to 80 years.The most commonly affected area of EMPD is the vulva;it accounts for 1%to 2%of vulvar malignancies.[1]The most common symptoms are chronic itching,vulvar pain,and erythema.However,symptoms can vary,and patients can remain asymptomatic for years.The typical feature of vulvar Paget’s disease(VPD)is an"icing cake effect"on the skin.[2]This disease is often misdiagnosed as eczema.Treatment delay is usually more than 2 years,and treatment can sometimes result in failure with a high recurrence rate.

关 键 词：PAGET ADENOCARCINOMA typically 

分 类 号：R736[医药卫生—肿瘤]