血管性血友病致反复失血性休克1例并文献复习  被引量:1

Recurrent Hemorrhagic Shock Induced by Von Willebrand Disease:A Case Report and Literature Review

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作  者:温贤浩[1] 唐雪[1] 刘海燕[1] 宪莹[1] 于洁[1] Wen Xianhao;Tang Xue;Liu Haiyan;Xian Ying;Yu Jie(Children’s Hospital of Chongqing Medical University,Ministry of Education Key Laboratory of Child Development and Disorders,China International Science and Technology Cooperation Base of Child Development and Critical Disorders,Key Laboratory of Pediatrics in Chongqing,Chongqing 400014,China)

机构地区:[1]重庆医科大学附属儿童医院,儿童发育疾病研究教育部重点实验室,儿童发育重大疾病国家国际科技合作基地,儿科学重庆市重点实验室,重庆400014

出  处:《儿科药学杂志》2022年第1期46-49,共4页Journal of Pediatric Pharmacy

摘  要:血管性血友病是常见的遗传性出血性疾病,临床表现多样化,其诊断及治疗仍面临挑战。本文报道血管性血友病致反复失血性休克1例,并进行相关文献复习,为深入认识血管性血友病,及时进行临床诊断及治疗提供参考。Von Willebrand disease is a kind of common genetic bleeding disorder with diverse clinical manifestations,its diagnosis and treatment remain challenging.This thesis reports a case of hemorrhagic shock induced by von Willebrand disease and reviews the related literature to provide reference for further understanding,timely clinical diagnosis and treatment of von Willebrand disease.

关 键 词:血管性血友病 临床表现 治疗 

分 类 号:R554.3[医药卫生—血液循环系统疾病]

 

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