Primary orbital monophasic synovial sarcoma with calcification:A case report  

作　　者：Ming-Yu Ren Jing Li Rui-Miao Li Yi-Xiang Wu Rui-Juan Han Chi Zhang 

机构地区：[1]Department of Orbital Disease and Ocular Tumor,Hebei Eye Hospital,Xingtai 054001,Hebei Province,China [2]Intensive Care Unit,Xingtai Third Hospital,Xingtai 054001,Hebei Province,China

出　　处：《World Journal of Clinical Cases》2022年第5期1623-1629,共7页世界临床病例杂志

基　　金：Supported by the Science and Technology Planning Project of Xingtai,No.2019ZC246.

摘　　要：BACKGROUND Synovial sarcoma is a malignant mesenchymal neoplasm with variable epithelial differentiation.Most synovial sarcoma cases are reported in young adults and can arise in any body site.Notably,primary orbital synovial sarcoma is rare.CASE SUMMARY An 8-year-old east Asian girl with 1-month history of gradual painless proptosis and lacrimation of the right eye was admitted.The patient presented with painless proptosis,downward eyeball displacement,and upward movement disorders.According to clinical manifestations,imaging examinations and postoperative immunohistochemical examinations,the diagnosis was monophasic synovial sarcoma with calcification.The patient underwent anterior orbitotomy procedure for removal of the right orbital mass under general anesthesia.The diagnosis of monophasic synovial sarcoma with calcification was confirmed finally through histological and immunohistochemical exam.The follow-up period was 6 mo,and no recurrence was observed during this period.CONCLUSION Primary orbital monophasic synovial sarcoma with calcification is a rare sarcoma,and clinical manifestations and imaging results are not specific.The tumor may present similar features as a benign tumor.Comprehensive analysis of clinical,radiological,and pathological findings is critically important for making the right diagnosis.Conventional treatment approach for synovial sarcoma is surgical resection with adjuvant or neoadjuvant radiotherapy,which is highly effective for localized tumors.

关 键 词：Orbital tumor Synovial sarcoma CALCIFICATION HISTOLOGICAL Case report 

分 类 号：R739.7[医药卫生—肿瘤]