以咽喉部肌无力为首发表现的儿童重症肌无力六例  

Six children with laryngopharyngeal myasthenia gravis as primary manifestation

作　　者：郑会晓 李宝广[1] 崔晓普 郭四仙 杨花芳 Zheng Huixiao;Li Baoguang;Cui Xiaopu;Guo Sixian;Yang Huafang(Department of Neurology,the Hebei Children's Hospital Affiliated to Hebei Medical University,Shijiazhuang 050031,China)

机构地区：[1]河北医科大学附属河北省儿童医院神经内科,石家庄050031

出　　处：《脑与神经疾病杂志》2022年第2期105-108,共4页Journal of Brain and Nervous Diseases

基　　金：河北省医学科学研究课题计划项目(20200177)。

摘　　要：目的提高临床医师对儿童期以咽喉部肌无力起病的重症肌无力(MG)临床表现的认识水平,做到及时诊断和个体化治疗。方法分析6例以咽喉部肌无力为主要表现的儿童期MG的诊断、鉴别诊断及治疗过程。结果在诊断儿童期MG明确后,给予规范治疗,病情迅速好转。结论以吞咽困难、构音障碍等咽喉肌病变表现为MG唯一或主要起病症状时,应尽早监测甲状腺功能情况,积极干预管理。Objective To improve clinicians’ cognitive level of manifestations of laryngopharyngeal myasthenia gravis(MG) as initial and primary manifestation in childhood,and promote diagnosis timely and individualized treatment.Methods Through analyzing the diagnose,antidiastole and treatment of six children with laryngopharyngeal MG.Rusults After the definite diagnosis of childhood MG,the children were given standardized treatment and the conditions were getting better quickly.Conclusion As laryngopharyngeal lesions,like dysphagia and dysarthria,are the exclusive initial and primary complains in MG,it is necessary to monitor thyroid function as soon as possible and intervene and manage MG positively.

关 键 词：重症肌无力 儿童 吞咽困难 声音嘶哑 自身免疫性甲状腺疾病 

分 类 号：R746.1[医药卫生—神经病学与精神病学]