遗传性原发性心律失常综合征的心房表型  

Atrial Phenotype of Inherited Primary Arrhythmia Syndrome

作　　者：杨丰菁 李翠兰[1] 刘文玲[1] YANG Fengjing;LI Cuilan;LIU Wenling(Department of Cardiology,Peking University People’s Hospital,Beijing 100044,China)

机构地区：[1]北京大学人民医院心内科,北京100044

出　　处：《心血管病学进展》2022年第3期193-197,共5页Advances in Cardiovascular Diseases

基　　金：国家自然科学基金(81270166)。

摘　　要：遗传性原发性心律失常综合征(IPAS)以恶性室性心律失常为主要特征,近年来其相关研究有了长足进展。由于共同的病理基质,IPAS患者也可发生房性心律失常,包括房性心动过速和心房颤动等,其心房颤动的患病率为2%~30%。不过,此类房性心律失常并未受到临床重视,其病因也知之甚少。因此,了解不同类型的IPAS伴发的房性心律失常发生率以及心房电异常,对其诊断与治疗有重要意义。现拟对不同类型IPAS患者伴发心房电异常的相关进展进行综述。Inherited primary arrhythmia syndrome(IPAS)is mainly characterized by malignant ventricular arrhythmia,and its related research has made great progress in recent years.Because of the common pathological matrix,IPAS patients can also produce atrial arrhythmias,including atrial tachycardia and atrial fibrillation.The prevalence of atrial fibrillation is from 2%to 30%.However,this kind of atrial arrhythmia has not received clinical attention,and its etiology is poorly understood.Therefore,understanding the incidence of atrial arrhythmias and atrial electrical abnormalities associated with different types of IPAS is of great significance for its diagnosis and treatment.This paper reviews the related progress of atrial electrical abnormalities in patients with different types of IPAS.

关 键 词：遗传性原发性心律失常 房性心律失常 心房颤动 

分 类 号：R54[医药卫生—心血管疾病]