Biliary atresia and congenital disorders of the extrahepatic bile ducts  

作　　者：Ali Islek Gokhan Tumgor 

机构地区：[1]Department of Pediatric Gastroenterology,Cukurova University School of Medicine,Adana 01320,Turkey

出　　处：《World Journal of Gastrointestinal Pharmacology and Therapeutics》2022年第4期33-46,共14页世界胃肠药理与治疗学杂志（英文版）（电子版）

摘　　要：Biliary atresia(BA)and choledochal cysts are diseases of the intrahepatic and extrahepatic biliary tree.While their exact etiopathogeneses are not known,they should be treated promptly due to the potential for irreversible parenchymal liver disease.A diagnosis of BA may be easy or complicated,but should not be delayed.BA is always treated surgically,and performing the surgery before the age of 2 mo greatly increases its effectiveness and extends the time until the need for liver transplantation arises.While the more common types of choledochal cysts require surgical treatment,some can be treated with endoscopic retrograde cholangiopancreatography.Choledochal cysts may cause recurrent cholangitis and the potential for malignancy should not be ignored.

关 键 词：Bilier atresia Choledochal cyst CHOLESTASIS Conjugated hyperbilirubinemia 

分 类 号：R726.5[医药卫生—儿科]