肝内窦前性非肝硬化性门静脉高压症的研究进展  

Research advances in non-cirrhotic intrahepatic presinusoidal portal hypertension

作　　者：夏帅 吴晓宁[1,2] 王冰琼 何志颖 尤红 XIA Shuai;WU Xiaoning;WANG Bingqiong;HE Zhiying;YOU Hong(Liver Research Center,Beijing Friendship Hospital,Capital Medical University,Beijing 100050,China;National Clinical Research Center for Digestive Diseases,Beijing 100050,China)

机构地区：[1]首都医科大学附属北京友谊医院肝病中心,北京100050 [2]国家消化系统疾病临床医学研究中心,北京100050

出　　处：《临床肝胆病杂志》2022年第7期1464-1468,共5页Journal of Clinical Hepatology

摘　　要：肝内窦前性非肝硬化性门静脉高压是非肝硬化性门静脉高压的一种类型,患者出现门静脉高压相关症状而无肝硬化病理证据,肝静脉压力梯度正常或轻微异常。因其病因复杂,极易漏诊、误诊,因此需要结合影像学与组织学检查明确诊断,适时启动降门静脉压治疗,预防性抗凝治疗的效果有待验证。Non-cirrhotic intrahepatic presinusoidal portal hypertension is a subtype of non-cirrhotic portal hypertension,and patients with this disease have the symptoms of portal hypertension and do not have the pathological evidence for liver cirrhosis,with normal or slightly abnormal hepatic venous pressure gradient.This disease is easily missed or misdiagnosed due to its complex etiology;therefore,radiological examination and histological examination should be combined in clinical practice to make a confirmed diagnosis,and related therapies should be initiated at the right time to reduce portal venous pressure.Further studies are needed to verify the efficacy of prophylactic anticoagulant therapy.

关 键 词：非肝硬化性门静脉高压 肝静脉闭塞性疾病 诊断 

分 类 号：R575.2[医药卫生—消化系统]