叶外型肺隔离症合并肺透明细胞瘤1例  

A Case of Extralobar Pulmonary Sequestration Complicated with Pulmonary Clear Cell Tumor

作　　者：吴德生[1] 陈秀禅 WU De-sheng;CHEN Xiu-chan(Department of Radiology,Guizhou Aerospace Hospital,Zunyi 563000,Guizhou Province,China;Department of Pathology,Guizhou Aerospace Hospital,Zunyi 563000,Guizhou Province,China)

机构地区：[1]贵州航天医院放射科,贵州遵义563000 [2]贵州航天医院病理科,贵州遵义563000

出　　处：《中国CT和MRI杂志》2022年第10期182-183,共2页Chinese Journal of CT and MRI

摘　　要：肺隔离症是一种少见的先天性肺部疾病,特征是肺组织由体循环参与供血,占先天性肺发育畸形的0.15%~6.40%,在临床上较为少见;肺透明细胞瘤更是非常罕见的肿瘤,2015年世界卫生组织将其归属为血管周上皮样肿瘤,多为良性,临床表现无特异性,常为单发,也可多发,影像表现多变,缺乏特异性,易造成误诊。在肺隔离症基础上并发肺透明细胞瘤更是鲜有报道,现将我院确诊的一列肺隔离症合并发透明细胞瘤的病例进行报道,旨在进一步加深对罕见病的认识,减少误诊,避免延误患者治疗时机。Pulmonary sequestration(PS)is a rare congenital lung disease characterized by the blood supply of the lung tissue from the systemic circulation,accounting for 0.15%to 6.40%of congenital lung developmental malformations,and is relatively rare in clinical practice.Clear cell tumor of the lung(CCTL)is a very rare tumor.In 2015,the World Health Organization classified it as perivascular epithelioid cell tumor(PEComa).Most of them are benign,with no specificity in clinical manifestations.They are often single or multiple,with variable imaging manifestations and lack of specificity,which is easy to cause misdiagnosis.There are few reports of CCTL on the basis of pulmonary sequestration.We report a case of PS combined with CCTL diagnosed in our hospital,in order to further deepen the understanding of the rare disease,reduce misdiagnosis,and avoid delaying the treatment opportunity of patients.

关 键 词：肺隔离症 肺透明细胞瘤 血管周上皮样肿瘤 

分 类 号：R734.2[医药卫生—肿瘤] R732.2[医药卫生—临床医学]