地中海贫血伴纵隔脊柱旁髓外造血1例及文献回顾  

Thalassemia with Extramedullary Hematopoiesis Near Mediastinal Spine: A Case Report and Literature Review

作　　者：黄蕾 吴新权 罗燕彤 李娜[3] HUANG Lei;WU Xin-quan;LUO Yan-tong;LI Na(Department of Guangzhou University of traditional Chinese Medicine,Shenzhen Clinical school,Shenzhen 518116,Guangdong Province,China;Department of Guangzhou University of traditional Chinese Medicine,Shenzhen 510405,Guangdong Province,China;Department of Longgang Central Hospital,Shenzhen 518116,Guangdong Province,China)

机构地区：[1]广州中医药大学深圳临床医学院,广东深圳518116 [2]广州中医药大学第一临床医学院,广东广州510405 [3]深圳市龙岗中心医院呼吸与危重症医学科,广东深圳518116

出　　处：《罕少疾病杂志》2022年第10期3-4,8,共3页Journal of Rare and Uncommon Diseases

摘　　要：目的探讨地中海贫血伴纵隔旁脊柱旁髓外造血的诊断、鉴别诊断及治疗。方法分析地中海贫血伴脊柱纵隔旁髓外造血一例并进行相关文献回顾。结果影像学检查考虑间皮瘤,患者未诉不适,为进一步明确诊断,在CT引导下穿刺,病理结果为髓外造血。结论若在血液病患者中发现多发对称性纵隔脊柱旁肿块,应考虑髓外造血在鉴别诊断中。治疗原发病、放射治疗及手术切除可视患者临床症状进行选择。Objective To investigate the diagnosis,differential diagnosis and treatment of thalassemia with paramediastinal paraspinal extramedullary hematopoiesis.Methods A case of thalassemia with paramediastinal extramedullary hematopoiesis was analyzed and related literatures were reviewed.Results Mesothelioma was considered in the imaging examination,and the patient did not complain of discomfort.In order to further confirm the diagnosis,CT-guided puncture was performed,and the pathological result was extramedullary hematopoiesis.Conclusions If multiple symmetrical mediastinal paraspinal masses are found in patients with hematological diseases,extramedullary hematopoiesis should be considered in the differential diagnosis.Treatment of primary disease,radiotherapy and surgical resection can be selected according to the clinical symptoms of patients.

关 键 词：地中海贫血 髓外造血 椎旁肿物 先天性溶血性疾病 

分 类 号：R556[医药卫生—血液循环系统疾病]