滤泡树突状细胞肉瘤的临床现状  

Clinical status of follicular dendritic cell sarcoma

作　　者：陈鼎浪 荆仁一 陈鼎之 苏智雄 CHEN Dinglang;JING Renyi;CHEN Dingzhi;SU Zhixiong(Department of General Practice,the Second Affiliated Hospital of Guangxi Medical University,Guangxi Zhuang Autonomous Region,Nanning 530007,China;Graduate School of Clinical Medicine,Shihezi University,Xinjiang Uygur Autonomous Region,Shihezi 832003,China;Department of General Surgery,Wuming Hospital of Guangxi Medical University,Guangxi Zhuang Autonomous Region,Nanning 530019,China)

机构地区：[1]广西医科大学第二附属医院全科医学科,广西南宁530007 [2]石河子大学临床医学院研究生院,新疆石河子832003 [3]广西医科大学附属武鸣医院普通外科,广西南宁530019

出　　处：《中国当代医药》2022年第27期42-45,共4页China Modern Medicine

摘　　要：滤泡树突状细胞肉瘤(FDCS)作为一种临床上可见的恶性肿瘤,由于对其发病机制、临床表现和诊治等方面尚未形成一个统一的描述,导致其在临床上极易被误诊、迟诊。由于发病位置的不同,很多患者常会出现不同的症状,如缓慢生长的无痛性肿块,包括腹痛、腹胀以及腹部包块为主的腹内表现以及全身症状。如果不能尽早诊断并采取科学的治疗措施,将会严重影响患者的身心健康。在现有关于FDCS的诊治记录中,基本以手术为主要手段,以控制患者的病情。因而本研究以综述角度出发,就FDCS的临床现状进行分析,力图描述FDCS的相关病因与发病机制、临床表现、影像学特征、病理学特征、鉴别诊断、治疗及预后等,旨在以此加深对FDCS的认识,并为未来对其发病机制的研究提供新的观点。Follicular dendritic cell sarcoma(FDCS),as a clinically visible malignant tumor,has not yet formed a unified description of its pathogenesis,clinical manifestations,diagnosis and treatment,which leads to its easy misdiagnosis and delayed diagnosis.Due to the different location of the disease,many patients often have different symptoms such as slow-growing painless mass,abdominal manifestations including abdominal pain,abdominal distension and abdominal mass,and constitutional symptoms.If not diagnosed as soon as possible and scientific treatment measures are taken,the physical and mental health of patients will be seriously affected.In the existing diagnosis and treatment records of FDCS,surgery is basically the main means to control the patients′condition.Therefore,this paper analyzes the current clinical situation of FDCS from the perspective of review and tries to describe the related etiology and pathogenesis,clinical manifestations,imaging features,pathological features,differential diagnosis,treatment,and prognosis of FDCS,to deepen our understanding of FDCS and provide a new perspective for future research on its pathogenesis.

关 键 词：滤泡 树突状细胞 肉瘤 透明血管型Castleman病 EB病毒 临床现状 

分 类 号：R73[医药卫生—肿瘤]