幼年性黄色肉芽肿继发儿童青光眼1例  

Glaucoma secondary with juvenile xanthogranuloma in children:a case report

作　　者：孔香云 张慧 乔春艳 Kong Xiangyun;Zhang Hui;Qiao Chunyan(Beijing Tongren Eye Center,Beijing Tongren Hospital,Capital Medical University,Beijing Institute of Ophthalmology,Beijing Key Laboratory of Ophthalmology&Visual Sciences,Beijing 100730,China;Department of Ophthalmology,Shandong Provincial Hospital Affiliated to Shandong First Medical University,Jinan 250021,China)

机构地区：[1]首都医科大学附属北京同仁医院北京同仁眼科中心北京市眼科研究所北京市眼科学与视觉科学重点实验室,北京100730 [2]山东第一医科大学附属省立医院眼科,济南250021

出　　处：《中华眼科杂志》2022年第10期796-798,共3页Chinese Journal of Ophthalmology

摘　　要：患儿为4个月男童,因家长发现其右眼不清亮27 d就诊。查体发现皮肤多发浅褐色斑丘疹,右眼压34.4 mmHg(1 mmHg=0.133 kPa),角膜增大水肿,房水血性混浊,颞下方角膜缘可见黄色的虹膜前粘连。超声生物显微镜示右眼前房角广泛粘连性关闭,局部虹膜增厚呈结节状。左眼查体未见异常。皮肤病损病理学检查后确诊为幼年性黄色肉芽肿,给予全身及局部糖皮质激素治疗及局部降眼压治疗病情好转,逐渐停药后眼压正常。现随访35个月,未用药眼压正常。A 4‑month‑old boy was admitted to the hospital after his parents noticed fog in his right eye for 27 days.Physical examination revealed multiple light brown macules on the skin.The intraocular pressure(IOP)of the right eye was 34.4 mmHg(1 mmHg=0.133kPa)and the corneal was enlarged and edema while the aqueous humor was cloudy with blood in the right eye.Yellow peripheral anterior synechia was seen on the temporal and inferior iris.Ultrasound biomicroscopy(UBM)showed extensive adhesion closure of the anterior chamber angle and the local thicken iris with the nodule.No obvious abnormality was observed in the left eye.It was confirmed as juvenile xanthogranuloma by skin lesion biopsy.IOP was normal after systemic and local therapy with corticosteroids and local IOP lowering medication.Follow up 35 months,IOP is normal without medication.

关 键 词：黄肉芽肿 青少年性 青光眼 前房出血 

分 类 号：R775[医药卫生—眼科]