Abernethy畸形肝脏结节的发病机制和诊疗进展  

Advances in the mechanisms,diagnoses and treatments of liver nodules in Abernethy malformation

作　　者：严佳虞 彭春辉[1] 王增萌[1] 吴东阳[1] 陈亚军[1] Yan Jiayu;Peng Chunhui;Wang Zengmeng;Wu Dongyang;Chen Yajun(Department of General Surgery,Beijing Children's Hospital,Capital Medical University,National Center of Children's Health,Beijing 100045,China)

机构地区：[1]国家儿童医学中心,首都医科大学附属北京儿童医院普外科,北京100045

出　　处：《中华小儿外科杂志》2022年第10期942-946,共5页Chinese Journal of Pediatric Surgery

摘　　要：Abernethy畸形是一种罕见的先天性血管畸形,门静脉血流于肝外经异常通道完全或部分绕过肝脏进入腔静脉系统,进而导致肺动脉高压、肝肺综合征、肝性脑病及肝脏结节等广泛临床表现。本文首先阐述Abernethy畸形肝脏结节的临床特点,然后对肝脏结节形成的发生机制及诊疗手段研究进展进行综述。Abernethy malformation is a congenital vascular anomaly in which portal blood completely or partially bypasses liver through a congenital portosystemic shunt,resulting in diverse clinical manifestations,such as pulmonary hypertension,hepatopulmonary syndrome,hepatic encephalopathy and liver nodules.Starting with clinical characteristics of liver nodules in Abernethy malformation,this review focused upon the formative mechanism of liver nodules and the latest advances of diagnosing and treating liver nodules in Abernethy malformation.

关 键 词：血管畸形 ABERNETHY畸形 肝脏结节 机制 诊断 治疗 

分 类 号：R575[医药卫生—消化系统]