儿童横纹肌样瘤的影像诊断  

Imaging diagnosis of rhabdoid tumorin children

作　　者：肖伟强 刘振清 吴倩倩 刘鸿圣 XIAO Weiqiang;LIU Zhenqing;WU Qianqian;LIU Hongsheng(Department of Radiology,Guangzhou Women and Children's Medical Center,Guangzhou 510623,China)

机构地区：[1]广州市妇女儿童医疗中心放射科,广东广州510623

出　　处：《实用放射学杂志》2022年第10期1685-1688,共4页Journal of Practical Radiology

摘　　要：目的探讨儿童横纹肌样瘤(RT)的影像学特点,提高对该病的认识与诊断水平。方法选取经病理证实RT且有术前影像学资料者87人(98例),总结其临床及影像特点。结果RT原发于肾最多(32例,32.65%),其次为脑实质(29例,29.59%)、脊髓或脊神经(11例,11.22%)和胸部(10例,10.20%)。瘤内囊变较多见(14例,14.3%),在肾内(8例)及脑内(6例)者囊变呈外周分布;钙化9例(9.2%),肾内(7例)者呈线状或结节状分布于外周,纵隔(1例)及肝内(1例)者呈结节状分布于肿瘤中心。结论RT的好发部位、肿瘤坏死囊变及钙化分布等表现均较具特点,综合患者年龄、全身多发、易转移易复发等特点,有助于正确诊断。Objective To investigate the imaging features of rhabdoid tumor(RT)in children,to improve the understanding and diagnosis level of RT.Methods The clinical and imaging data of 87 children(98 cases)with RT proved by pathology were selected and summarized.Results RT mainly occurred in the kidney(32 cases,32.65%),followed by brain parenchyma(29 cases,29.59%),spinal or spinal nerve(11 cases,11.22%)and thorax(10 cases,10.20%).Intratumoral cysts were common(14 cases,14.3%),the cysts of kidney mass(8 cases)and brain mass(6 cases)were peripherally distributed;calcification was shown in 9 cases(9.2%),including the cases of kidney(7 cases)were cord-like,nodular-like and peripherally distributed,the cases of mediastinum(1 case)and liver(1 case)were nodular-like and central distributed.Conclusion The location of RT,the distribution of necrosis,cystic degeneration and calcification in the mass are differential characteristics,which are helpful for the correct diagnosis of RT,combined with the patient's age,the characteristics suchas multi-sites,metastasis and recurrence.

关 键 词：儿童 横纹肌样瘤 计算机体层成像 磁共振成像 

分 类 号：R738.6[医药卫生—肿瘤] R814.42[医药卫生—临床医学] R445.2