Primary peritoneal hemangioendothelioma simulating an ovarian cyst:A case report and review of literature  

作　　者：Claudio Spinelli Marco Ghionzoli Silvia Strambi 

机构地区：[1]Pediatric and Adolescent Surgery Division,Department of Surgical,Medical,Molecular Pathology and of the Critic Area,University of Pisa,Pisa 56126,Italy

出　　处：《World Journal of Obstetrics and Gynecology》2022年第4期40-46,共7页世界妇产科杂志

摘　　要：BACKGROUND Epithelioid hemangioendothelioma(EHE)is an extremely rare tumor with a prevalence of one in a million and a very heterogenous spectrum of disease that varies from an indolent to a metastasizing aggressive disease,with the liver,lung and bone being the primarily involved organs.Peritoneal forms of EHE are even rare,and only 12 cases have been reported to date in the literature.CASE SUMMARY A 66-year-old female came to our attention complaining low abdominal and perineal pain.Magnetic resonance imaging examination showed a 52 mm×58 mm×32 mm cystic mass with some smooth septa,simulating an ovarian cyst.Explorative laparoscopy demonstrated the presence of a peritoneal mass of augmented consistency connected with a sigmoid epiploic appendix in the right side of the Pouch of Douglas,that was surgically removed.Histological examination revealed a primitive peritoneafl hemangioendothelioma.The patient easily recovered from surgery with no residual pain or discomfort.She is regularly attending a 3-years follow-up that is negative for local recurrence of disease or distant metastases.CONCLUSION Peritoneal form of EHE often simulates masses of other nature,as in our case.Given its unspecific clinical and radiological presentation,patients are often forced to a large series of tests and examinations before reaching a definitive diagnosis,that can only histologically made.The possibility of EHE should always be considered in case of unexplained chronic abdominal pain associated to a non-specific mass.

关 键 词：Epithelioid hemangioendothelioma Peritoneal hemangioendothelioma Peritoneal tumor HEMANGIOENDOTHELIOMA Unusual presentation Case report 

分 类 号：R73[医药卫生—肿瘤]