Blau综合征成年患者抗青光眼手术后并发白内障手术治疗1例并文献复习  

Surgical treatment of a cataract complicated by anti-glaucoma surgery in an adult patient with Blau syndrome

作　　者：石博影 梁皓[1] 李一洪 唐东永[1] SHI Boying;LIANG Hao;LI Yihong;TANG Dongyong(Department of Ophthalmology,The First Affiliated Hospital of Guangxi Medical University,Nanning 530021,Guangxi,China)

机构地区：[1]广西医科大学第一附属医院眼科,广西南宁530021

出　　处：《山东大学耳鼻喉眼学报》2022年第6期60-65,共6页Journal of Otolaryngology and Ophthalmology of Shandong University

基　　金：国家自然科学基金(82103101219038D)。

摘　　要：目的 观察1例既往确诊Blau综合征11年的成年患者先后出现多种眼部病变后手术治疗的效果,为规范化诊疗、围手术期管理提供思路及参考。方法 通过报告1例Blau综合征成年患者病程中先后出现双眼葡萄膜炎、双眼继发性闭角型青光眼、双眼并发性白内障,并分别于2016年左眼行青光眼阀管植入+异体巩膜移植+前房成形+瞳孔再造术、2020年行左眼超声乳化白内障吸除联合人工晶状体植入及虹膜周边切除术的病例,分析和总结Blau综合征患者并发性白内障的临床诊疗思维、围手术期管理等。结果 患者术后3个月、6个月复查视力明显提高,眼压正常,前房中深,虹膜周切口通畅,人工晶状体位正。结论 Blau综合征患者的眼部病变需要早期、持续的观察和监测,及时给予规范合理的诊疗后患者可保留足够的视力以保障生活质量。Objective To observe the effect of surgical treatment of an adult patient with BLAU syndrome diagnosed in the past11years who developed a variety of ocular lesions successively,providing guidance and reference for standardized diagnosis and treatment,and perioperative management. Methods This is a case report of1adult BLAU syndrome patient who,in the course of the disease,developed binocular uveitis,binocular secondary angle-closure glaucoma,and binocular concurrent cataract. In2016his left eye received a glaucoma valve tube implantation,allograft sclera transplantation,anterior chamber remodeling,and pupil reconstruction. In2020,phacoemulsification of the left eye combined with intraocular lens implantation and peri-iridectomy were performed. In this paper an analysis and summary of the clinical diagnosis,treatment conception and perioperative management of concurrent cataracts in a patient with Blau syndrome is presented. Results Three and six months after the operation,the patient’s visual acuity improved significantly,her intraocular pressure returned to normal,the anterior chamber was deep,the peri-iris incision was smooth,and the intraocular lens was in the right position. Conclusion Ocular lesions of patients with Blau syndrome require early and continuous observation and monitoring. After timely,standardized,and well-considered diagnosis and treatment,patients can maintain enough vision to sustain their quality of life.

关 键 词：Blau综合征 葡萄膜炎 白内障 青光眼 超声乳化术 

分 类 号：R775.3[医药卫生—眼科]