喉原发性骨外尤文肉瘤1例报道并文献复习  

A case of extraskeletal Ewing’s sarcoma of the larynx and literature review

作　　者：刘佳 吴求吉[1] 钟亚华[1] Jia LIU;Qiu-Ji WU;Ya-Hua ZHONG(Department of Radiation and Medical Oncology,Zhongnan Hospital of Wuhan University,Wuhan 430071,China)

机构地区：[1]武汉大学中南医院肿瘤放化疗科,武汉430071

出　　处：《数理医药学杂志》2023年第2期150-154,共5页Journal of Mathematical Medicine

基　　金：国家自然科学基金应急管理项目(81641116)。

摘　　要：回顾性分析1例喉原发性骨外尤文肉瘤患者的临床资料,并回顾相关文献。1名11岁男童因急性呼吸窘迫就诊,急诊行气管切开术+喉肿物活检术,免疫组化及分子病理确诊为喉尤文肉瘤。结合病史考虑患者局部肿瘤复发,采用放化疗为主的综合治疗,随访6个月无复发及转移。喉骨外尤文肉瘤极为罕见,临床表现缺乏特异性,早期诊断困难,多采用综合治疗方案。本病容易复发及转移,预后不佳。e clinical data of a patient with primary extraskeletal Ewing’s sarcoma of the larynx were retrospectively analyzed, and relevant literature was reviewed. An 11-yearold boy presented with acute respiratory distress, underwent emergency tracheotomy and laryngeal mass biopsy, and the diagnosis of laryngeal Ewing sarcoma was confirmed by immunohistochemistry and molecular pathology. Recurrence of tumors was considered, and the treatment was a combination of radiotherapy and chemotherapy, with no recurrence or metastasis at 6-month follow-up. The extraskeletal Ewing’s sarcoma, which is rare arising from the larynx, lacks specificity in clinical presentation and early diagnosis is difficult. Individualized comprehensive treatment should be emphasized. The disease is prone to recurrence and metastasis, resulting in poor prognosis.

关 键 词：骨外尤文肉瘤 喉 

分 类 号：R739.65[医药卫生—肿瘤]