先天性颞骨胆脂瘤的诊断和治疗  

Diagnosis and treatment of congenital temporal bone cholesteatoma

作　　者：李雅兰 周函[1] 陆玲[1] 戴艳红[1] 张小莉[1] 陈杰[1] 俞晨杰[1] 钱晓云[1] LI Yalan;ZHOU Han;LU Ling;DAI Yanhong;ZHANG Xiaoli;CHEN Jie;YU Chenjie;QIAN Xiaoyun(Department of Otolaryngology Head and Neck Surgery,Nanjing Drum Tower Hospital,the Affiliated Hospital of Nanjing University Medical School,Jiangsu Provincial Key Medical Discipline,Research Institute of Otolaryngology,Nanjing,210008,China)

机构地区：[1]南京大学医学院附属鼓楼医院耳鼻咽喉头颈外科、江苏省医学重点学科、南京鼓楼医院耳鼻咽喉研究所,南京210008

出　　处：《临床耳鼻咽喉头颈外科杂志》2023年第3期186-189,196,共5页Journal of Clinical Otorhinolaryngology Head And Neck Surgery

基　　金：国家自然科学基金(No:82192862,82101223);中国博士后科学基金(No:2020M681561)。

摘　　要：先天性颞骨胆脂瘤是耳鼻喉科的罕见疾病,具有侵袭性,可能导致包括听力损失(传导性或感音神经性)、颞骨破坏以及颅内侵犯等严重并发症。本文回顾了先天性颞骨胆脂瘤的临床表现、影像学特征、分期和目前的治疗方案,以期提高认识,及时进行手术治疗,避免胆脂瘤对于颞骨及周围结构的破坏,从而减少并发症。Congenital temporal bone cholesteatoma is a rare lesion in otolaryngology.The disease is locally invasive and may lead to significant complications, including hearing loss(conductive or sensorineural), temporal bone destruction and intracranial invasion. This article reviews the characteristic symptoms of congenital temporal bone cholesteatoma, testing and imaging of the disease, stage and the current treatment options in order to promote awareness to this rare disease entity and perform early surgical treatment, effectively avoid the destruction of the temporal bone and its surrounding structures, thereby reducing the occurrence of complications. By improving the understanding of the disease and performing early surgical treatment, the destruction of the temporal bone and its surrounding structures can be effectively avoided, thereby reducing the occurrence of complications.

关 键 词：先天性颞骨胆脂瘤 中耳 岩骨 内镜 

分 类 号：R739.61[医药卫生—肿瘤]