丙酸血症患儿行亲体肝移植的术后护理  

Postoperative nursing of children with propionic acidemia undergoing parent-child liver transplantation

作　　者：王燕[1] 卢芳燕 王芳[1] WANG Yan;LU Fangyan;WANG Fang

机构地区：[1]浙江大学医学院附属第一医院肝移植中心,杭州市310003

出　　处：《中华急危重症护理杂志》2023年第4期347-349,共3页Chinese Journal of Emergency and Critical Care Nursing

基　　金：浙江省中医药科学研究基金项目(2022ZA093)。

摘　　要：总结2例丙酸血症患儿行亲体肝移植的术后护理体会。针对该组患儿病情累及多器官、代谢紊乱、血管并发症及镇静难度大等问题,护理要点:监测重要器官功能,及时汇报异常情况;维持酸碱平衡,警惕发生酸中毒和高血氨;严格执行抗凝治疗,降低血管相关并发症;有效镇静护理,预防发生抽搐;准确服用免疫抑制剂,预防急性排斥反应;特殊配方饮食,控制蛋白质摄入等。经过积极治疗和精心护理,2例患儿术后康复出院,随访1年余,预后良好。The postoperative nursing experience of two children with propionic acidemia undergoing parent-child liver transplantation was summarized.In view of the problems of multiple organ involvements,metabolic disorders,vascular complications and difficulty of sedation in this group of children,the following interventions were adopted,including monitoring the function of important organs and reporting abnormal conditions timely,the maintain of acidbase balance and being cautious of acidosis and hyperammonemia,strict implementation of anticoagulation therapy to reduce vascular-related complications,effective sedative care to prevent the occurrence of convulsions,accurate administration of immunosuppressants to prevent acute rejection,special formulated diets and control of protein intake.After active treatment and meticulous care,two children were discharged from the hospital after surgery and followed up for more than 1 year with a good prognosis.

关 键 词：丙酸血症 儿童 肝移植 重症监护 

分 类 号：R473.72[医药卫生—护理学]